Class information for:
Level 1: TDP 43//C9ORF72//TARDBP

Basic class information
ID Publications Average number
of references		 Avg. shr. active
ref. in WoS
5539 1544 49.4 92%


Bar chart of Publication_year

Last years might be incomplete

Classes in level above (level 2)


ID, lev.
above		 Publications Label for level above
799 11424 AMYOTROPHIC LATERAL SCLEROSIS//SPINAL MUSCULAR ATROPHY//MOTOR NEURON DISEASE

Terms with highest relevance score


Rank Term Type of term Relevance score
(tfidf)		 Class's shr.
of term's tot.
occurrences		 Shr. of publ.
in class containing
term		 Num. of
publ. in
class
1 TDP 43 Author keyword 290 61% 20% 305
2 C9ORF72 Author keyword 229 80% 9% 143
3 TARDBP Author keyword 74 84% 3% 41
4 FUS Author keyword 67 52% 6% 90
5 FTLD Author keyword 48 57% 4% 57
6 FUS TLS Author keyword 44 85% 1% 23
7 FUSED IN SARCOMA Author keyword 40 82% 1% 23
8 FRONTOTEMPORAL LOBAR DEGENERATION Author keyword 30 22% 8% 119
9 BASOPHILIC INCLUSION Author keyword 24 91% 1% 10
10 TAR DNA BINDING PROTEIN 43 Author keyword 22 66% 1% 21

Web of Science journal categories

Author Key Words


Rank Web of Science journal category Relevance score
(tfidf)		 Class's shr.
of term's tot.
occurrences		 Shr. of publ.
in class containing
term		 Num. of
publ. in
class		 LCSH search Wikipedia search
1 TDP 43 290 61% 20% 305 Search TDP+43 Search TDP+43
2 C9ORF72 229 80% 9% 143 Search C9ORF72 Search C9ORF72
3 TARDBP 74 84% 3% 41 Search TARDBP Search TARDBP
4 FUS 67 52% 6% 90 Search FUS Search FUS
5 FTLD 48 57% 4% 57 Search FTLD Search FTLD
6 FUS TLS 44 85% 1% 23 Search FUS+TLS Search FUS+TLS
7 FUSED IN SARCOMA 40 82% 1% 23 Search FUSED+IN+SARCOMA Search FUSED+IN+SARCOMA
8 FRONTOTEMPORAL LOBAR DEGENERATION 30 22% 8% 119 Search FRONTOTEMPORAL+LOBAR+DEGENERATION Search FRONTOTEMPORAL+LOBAR+DEGENERATION
9 BASOPHILIC INCLUSION 24 91% 1% 10 Search BASOPHILIC+INCLUSION Search BASOPHILIC+INCLUSION
10 TAR DNA BINDING PROTEIN 43 22 66% 1% 21 Search TAR+DNA+BINDING+PROTEIN+43 Search TAR+DNA+BINDING+PROTEIN+43

Key Words Plus


Rank Web of Science journal category Relevance score
(tfidf)		 Class's shr.
of term's tot.
occurrences		 Shr. of publ.
in class containing
term		 Num. of
publ. in
class
1 FRONTOTEMPORAL LOBAR DEGENERATION 325 36% 46% 717
2 NUCLEAR FACTOR TDP 43 189 77% 8% 127
3 TARDBP MUTATIONS 176 79% 7% 113
4 TDP 43 166 52% 15% 228
5 HEXANUCLEOTIDE REPEAT 116 43% 13% 204
6 CFTR EXON 9 107 84% 4% 58
7 FTD 101 61% 7% 108
8 TAR DNA BINDING 91 85% 3% 47
9 GGGGCC REPEAT 82 88% 2% 38
10 GGGGCC HEXANUCLEOTIDE REPEAT 77 96% 2% 24

Journals


Rank Web of Science journal category Relevance score
(tfidf)		 Class's shr.
of term's tot.
occurrences		 Shr. of publ.
in class containing
term		 Num. of
publ. in
class
1 AMYOTROPHIC LATERAL SCLEROSIS AND FRONTOTEMPORAL DEGENERATION 3 11% 2% 25

Reviews


Title Publ. year Cit. Active references % act. ref.
to same field
State of play in amyotrophic lateral sclerosis genetics 2014 102 89 54%
C9orf72 expansions in frontotemporal dementia and amyotrophic lateral sclerosis 2015 4 116 89%
Converging Mechanisms in ALS and FTD: Disrupted RNA and Protein Homeostasis 2013 121 241 60%
The changing scene of amyotrophic lateral sclerosis 2013 155 228 42%
Gains or losses: molecular mechanisms of TDP43-mediated neurodegeneration 2012 96 141 78%
Sporadic and hereditary amyotrophic lateral sclerosis (ALS) 2015 4 59 49%
The neuropathology associated with repeat expansions in the C9ORF72 gene 2014 17 65 83%
Stress granules as crucibles of ALS pathogenesis 2013 88 93 56%
TDP-43 and FUS/TLS: emerging roles in RNA processing and neurodegeneration 2010 268 251 66%
TDP-43 and FUS in amyotrophic lateral sclerosis and frontotemporal dementia 2010 236 191 67%

Address terms


Rank Address term Relevance score
(tfidf)		 Class's shr.
of term's tot.
occurrences		 Shr. of publ.
in class containing
term		 Num. of
publ. in
class
1 DIAG CURE RARE DIS 15 88% 0.5% 7
2 TRANSLAT NEUROPATHOL 15 88% 0.5% 7
3 REFERENCE MALAD RA SLA 11 69% 0.6% 9
4 NEUROMUSCULAR DIS GRP 10 50% 0.9% 14
5 NORTHCOTT NEUROSCI 9 38% 1.2% 19
6 NEUROPATHOL CELL BIOL 7 56% 0.6% 9
7 PAUL CASTAIGNE 5 63% 0.3% 5
8 MED COUNCIL NEURODEGENERAT 5 50% 0.5% 7
9 UNITE NEUROL COMPORTEMENTALE DEGENERAT 5 50% 0.5% 7
10 RITA LEVI MONTALCINI NEUROSCI 5 31% 0.8% 13

Related classes at same level (level 1)


Rank Relatedness score Related classes
1 0.0000186315 FRONTOTEMPORAL DEMENTIA//PRIMARY PROGRESSIVE APHASIA//FRONTOTEMPORAL LOBAR DEGENERATION
2 0.0000173035 PRIMARY LATERAL SCLEROSIS//BUNINA BODY//MOTOR NEURON DISEASE
3 0.0000144102 AMYOTROPHIC LATERAL SCLEROSIS//SOD1//ALS
4 0.0000079302 CELLULAR NEUROL//PROTEOPATHY//PRION LIKE AGGREGATION
5 0.0000071164 AMYOTROPHIC LATERAL SCLEROSIS//AMYOTROPHIC LATERAL SCLEROSIS AND FRONTOTEMPORAL DEGENERATION//MOTOR NEURON DISEASE
6 0.0000058565 NEURONAL INTRANUCLEAR INCLUSION DISEASE//INTRANUCLEAR INCLUSION BODY DISEASE//NEURONAL INTRANUCLEAR HYALINE INCLUSION DISEASE
7 0.0000057974 P54NRB//POLYPYRIMIDINE TRACT BINDING PROTEIN ASSOCIATED SPLICING FACTOR//MATRIN 3
8 0.0000055689 OXYSTEROL BINDING PROTEIN//OXYSTEROL BINDING PROTEINS//OSBP
9 0.0000048902 PROGRANULIN//ACROGRANIN//EPITHELIN
10 0.0000041118 DECAPPING//P BODIES//CCR4 NOT