Class information for:
Level 1: PURINE NUCLEOSIDE PHOSPHORYLASE DEFICIENCY//ADENOSINE DEAMINASE//CECR1

Basic class information

ID Publications Average number
of references
Avg. shr. active
ref. in WoS
4712 1665 31.1 47%



Bar chart of Publication_year

Last years might be incomplete

Classes in level above (level 2)



ID, lev.
above
Publications Label for level above
1233 8561 DEOXYCYTIDINE KINASE//PURINE NUCLEOSIDE PHOSPHORYLASE//NUCLEOSIDE TRANSPORT

Terms with highest relevance score



Rank Term Type of term Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
1 PURINE NUCLEOSIDE PHOSPHORYLASE DEFICIENCY Author keyword 30 100% 1% 12
2 ADENOSINE DEAMINASE Author keyword 29 17% 9% 153
3 CECR1 Author keyword 12 86% 0% 6
4 SHIFTING SPECIFICITY MODEL Author keyword 11 100% 0% 6
5 ADGF Author keyword 9 83% 0% 5
6 ADENOSINE DEAMINASE DEFICIENCY Author keyword 6 40% 1% 12
7 ADENOSINE DEAMINASE INHIBITORS Author keyword 4 50% 0% 6
8 PEG ADA Author keyword 3 57% 0% 4
9 INSECT DERIVED GROWTH FACTOR Author keyword 3 100% 0% 3
10 COFORMYCIN Author keyword 3 50% 0% 4

Web of Science journal categories

Author Key Words



Rank Web of Science journal category Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
LCSH search Wikipedia search
1 PURINE NUCLEOSIDE PHOSPHORYLASE DEFICIENCY 30 100% 1% 12 Search PURINE+NUCLEOSIDE+PHOSPHORYLASE+DEFICIENCY Search PURINE+NUCLEOSIDE+PHOSPHORYLASE+DEFICIENCY
2 ADENOSINE DEAMINASE 29 17% 9% 153 Search ADENOSINE+DEAMINASE Search ADENOSINE+DEAMINASE
3 CECR1 12 86% 0% 6 Search CECR1 Search CECR1
4 SHIFTING SPECIFICITY MODEL 11 100% 0% 6 Search SHIFTING+SPECIFICITY+MODEL Search SHIFTING+SPECIFICITY+MODEL
5 ADGF 9 83% 0% 5 Search ADGF Search ADGF
6 ADENOSINE DEAMINASE DEFICIENCY 6 40% 1% 12 Search ADENOSINE+DEAMINASE+DEFICIENCY Search ADENOSINE+DEAMINASE+DEFICIENCY
7 ADENOSINE DEAMINASE INHIBITORS 4 50% 0% 6 Search ADENOSINE+DEAMINASE+INHIBITORS Search ADENOSINE+DEAMINASE+INHIBITORS
8 PEG ADA 3 57% 0% 4 Search PEG+ADA Search PEG+ADA
9 INSECT DERIVED GROWTH FACTOR 3 100% 0% 3 Search INSECT+DERIVED+GROWTH+FACTOR Search INSECT+DERIVED+GROWTH+FACTOR
10 COFORMYCIN 3 50% 0% 4 Search COFORMYCIN Search COFORMYCIN

Key Words Plus



Rank Web of Science journal category Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
1 ERYTHRO 9 2 HYDROXY 3 NONYLADENINE 42 94% 1% 15
2 ADA DEFICIENCY 12 75% 1% 9
3 2 DEOXYCOFORMYCIN 12 27% 2% 38
4 DEOXYCOFORMYCIN 10 30% 2% 28
5 DEOXYADENOSINE METABOLISM 9 67% 0% 8
6 INOSINE DERIVATIVES 6 100% 0% 4
7 SINGLE HYDROXYL GROUP 6 50% 0% 8
8 NUCLEOSIDE PHOSPHORYLASE DEFICIENCY 5 30% 1% 15
9 DEOXYADENOSINE 5 14% 2% 33
10 2 DEOXYCOFORMYCIN TREATMENT 4 67% 0% 4

Journals

Reviews



Title Publ. year Cit. Active references % act. ref.
to same field
Moonlighting Adenosine Deaminase: A Target Protein for Drug Development 2015 1 348 28%
How I treat ADA deficiency 2009 60 42 45%
Adenosine deaminase: Functional implications and different classes of inhibitors 2001 133 167 66%
Management options for adenosine deaminase deficiency; proceedings of the EBMT satellite workshop (Hamburg, March 2006) 2007 32 24 58%
Recent advances in understanding and managing adenosine deaminase and purine nucleoside phosphorylase deficiencies 2013 7 63 62%
Enzymatic and extraenzymatic role of ecto-adenosine deaminase in lymphocytes 1998 108 82 46%
Cell surface adenosine deaminase: Much more than an ectoenzyme 1997 134 77 42%
Genotype is an important determinant of phenotype in adenosine deaminase deficiency 2003 38 47 66%
Adenosine Deaminase in the Modulation of Immune System and its Potential as a Novel Target for Treatment of Inflammatory Disorders 2012 16 199 40%
2'-DEOXYCOFORMYCIN (PENTOSTATIN) FOR LYMPHOID MALIGNANCIES - RATIONAL DEVELOPMENT OF AN ACTIVE NEW DRUG 1988 95 77 69%

Address terms



Rank Address term Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ.
in class
1 ANIM ENDOCRINOL METAB 2 67% 0.1% 2
2 INFECT IMMUN INJURY REPAIR PROGRAM 1 17% 0.3% 5
3 BUNIATYAN BIOCHEM 1 33% 0.1% 2
4 ANIM ENDOCRINOL METABOL 1 50% 0.1% 1
5 CATTEDRA PEDIAT PREVENT SOCIALE 1 50% 0.1% 1
6 CHILDRENS HOSP LUND 1 50% 0.1% 1
7 CHTSB 1 50% 0.1% 1
8 CIRID UMR 5164 1 50% 0.1% 1
9 G KH BUNYATYAN BIOCHEM 1 50% 0.1% 1
10 IDC MUNCHEN 1 50% 0.1% 1

Related classes at same level (level 1)



Rank Relatedness score Related classes
1 0.0000143212 DRUG DESIGN SYNTH//GUANINE DEAMINASE//GUANASE
2 0.0000102012 CN II//PYRIMIDINE 5 NUCLEOTIDASE//5 NUCLEOTIDASES
3 0.0000096264 CYTIDINE DEAMINASE//ANTIBIOTIC FUNGICIDE//BLASTICIDIN S DEAMINASE
4 0.0000091732 OMENN SYNDROME//SEVERE COMBINED IMMUNODEFICIENCY//T CELL LYMPHOPENIA
5 0.0000083466 AMP DEAMINASE//AMPD1 GENE//MYOADENYLATE DEAMINASE DEFICIENCY
6 0.0000082212 TUBERCULOUS PLEURISY//TRANSUDATES//PLEURAL EFFUSION
7 0.0000082204 CLOFARABINE//CANC THER EUT IMMUNOL//NELARABINE
8 0.0000079496 PURINE NUCLEOSIDE PHOSPHORYLASE//NUCLEOSIDE PHOSPHORYLASES//CARBOHYDRATE CHEM TEAM
9 0.0000055067 NEW ENGLAND INFLAMMAT TISSUE PROTECT//MUCOSAL INFLAMMAT PROGRAM//ADENOSINE RECEPTORS
10 0.0000051391 NTPDASE//ATP DIPHOSPHOHYDROLASE//ECTO ATPASE