Class information for:
Level 1: HEMOPHAGOCYTIC LYMPHOHISTIOCYTOSIS//HEMOPHAGOCYTIC SYNDROME//HAEMOPHAGOCYTIC LYMPHOHISTIOCYTOSIS

Basic class information
ID Publications Average number
of references		 Avg. shr. active
ref. in WoS
4317 1732 26.8 80%


Bar chart of Publication_year

Last years might be incomplete

Classes in level above (level 2)


ID, lev.
above		 Publications Label for level above
1918 5294 HEMOPHAGOCYTIC LYMPHOHISTIOCYTOSIS//JUVENILE IDIOPATHIC ARTHRITIS//ADULT ONSET STILLS DISEASE

Terms with highest relevance score


Rank Term Type of term Relevance score
(tfidf)		 Class's shr.
of term's tot.
occurrences		 Shr. of publ.
in class containing
term		 Num. of
publ. in
class
1 HEMOPHAGOCYTIC LYMPHOHISTIOCYTOSIS Author keyword 419 76% 17% 297
2 HEMOPHAGOCYTIC SYNDROME Author keyword 204 58% 14% 235
3 HAEMOPHAGOCYTIC LYMPHOHISTIOCYTOSIS Author keyword 125 88% 3% 59
4 FAMILIAL HEMOPHAGOCYTIC LYMPHOHISTIOCYTOSIS Author keyword 125 87% 4% 61
5 HEMOPHAGOCYTOSIS Author keyword 112 59% 7% 124
6 MACROPHAGE ACTIVATION SYNDROME Author keyword 108 63% 6% 109
7 HAEMOPHAGOCYTIC SYNDROME Author keyword 42 64% 2% 41
8 HEMOPHAGOCYTIC LYMPHOHISTIOCYTOSIS HLH Author keyword 39 80% 1% 24
9 LYMPHOHISTIOCYTOSIS Author keyword 35 76% 1% 25
10 PERFORIN GENE Author keyword 26 87% 1% 13

Web of Science journal categories

Author Key Words


Rank Web of Science journal category Relevance score
(tfidf)		 Class's shr.
of term's tot.
occurrences		 Shr. of publ.
in class containing
term		 Num. of
publ. in
class		 LCSH search Wikipedia search
1 HEMOPHAGOCYTIC LYMPHOHISTIOCYTOSIS 419 76% 17% 297 Search HEMOPHAGOCYTIC+LYMPHOHISTIOCYTOSIS Search HEMOPHAGOCYTIC+LYMPHOHISTIOCYTOSIS
2 HEMOPHAGOCYTIC SYNDROME 204 58% 14% 235 Search HEMOPHAGOCYTIC+SYNDROME Search HEMOPHAGOCYTIC+SYNDROME
3 HAEMOPHAGOCYTIC LYMPHOHISTIOCYTOSIS 125 88% 3% 59 Search HAEMOPHAGOCYTIC+LYMPHOHISTIOCYTOSIS Search HAEMOPHAGOCYTIC+LYMPHOHISTIOCYTOSIS
4 FAMILIAL HEMOPHAGOCYTIC LYMPHOHISTIOCYTOSIS 125 87% 4% 61 Search FAMILIAL+HEMOPHAGOCYTIC+LYMPHOHISTIOCYTOSIS Search FAMILIAL+HEMOPHAGOCYTIC+LYMPHOHISTIOCYTOSIS
5 HEMOPHAGOCYTOSIS 112 59% 7% 124 Search HEMOPHAGOCYTOSIS Search HEMOPHAGOCYTOSIS
6 MACROPHAGE ACTIVATION SYNDROME 108 63% 6% 109 Search MACROPHAGE+ACTIVATION+SYNDROME Search MACROPHAGE+ACTIVATION+SYNDROME
7 HAEMOPHAGOCYTIC SYNDROME 42 64% 2% 41 Search HAEMOPHAGOCYTIC+SYNDROME Search HAEMOPHAGOCYTIC+SYNDROME
8 HEMOPHAGOCYTIC LYMPHOHISTIOCYTOSIS HLH 39 80% 1% 24 Search HEMOPHAGOCYTIC+LYMPHOHISTIOCYTOSIS+HLH Search HEMOPHAGOCYTIC+LYMPHOHISTIOCYTOSIS+HLH
9 LYMPHOHISTIOCYTOSIS 35 76% 1% 25 Search LYMPHOHISTIOCYTOSIS Search LYMPHOHISTIOCYTOSIS
10 PERFORIN GENE 26 87% 1% 13 Search PERFORIN+GENE Search PERFORIN+GENE

Key Words Plus


Rank Web of Science journal category Relevance score
(tfidf)		 Class's shr.
of term's tot.
occurrences		 Shr. of publ.
in class containing
term		 Num. of
publ. in
class
1 LYMPHOHISTIOCYTOSIS 360 68% 18% 314
2 ERYTHROPHAGOCYTIC LYMPHOHISTIOCYTOSIS 178 94% 4% 63
3 PERFORIN GENE MUTATIONS 129 100% 2% 36
4 FAMILIAL ERYTHROPHAGOCYTIC LYMPHOHISTIOCYTOSIS 64 86% 2% 32
5 FAMILIAL HEMOPHAGOCYTIC LYMPHOHISTIOCYTOSIS 60 45% 6% 102
6 MALIGNANT HISTIOCYTOSIS 60 30% 10% 170
7 MACROPHAGE ACTIVATION SYNDROME 55 36% 7% 122
8 HISTIOCYTIC MEDULLARY RETICULOSIS 46 82% 2% 27
9 A91V 44 88% 1% 21
10 KILLER CELL DYSFUNCTION 44 74% 2% 32

Journals

Reviews


Title Publ. year Cit. Active references % act. ref.
to same field
HLH-2004: Diagnostic and therapeutic guidelines for hemophagocytic lymphohistiocytosis 2007 769 51 92%
Familial and Acquired Hemophagocytic Lymphohistiocytosis 2012 103 56 91%
Macrophage activation syndrome in Kawasaki Disease: More common than we thought? 2015 2 19 84%
Macrophage activation syndrome as part of systemic juvenile idiopathic arthritis: diagnosis, genetics, pathophysiology and treatment 2012 58 112 62%
Hemophagocytic Lymphohistiocytosis An Update on Diagnosis and Pathogenesis 2013 27 121 81%
Hemophagocytic lymphohistiocytosis: updates and evolving concepts 2012 33 33 88%
Advances in understanding the pathogenesis of HLH 2013 24 110 85%
Hemophagocytic Syndrome and Critical Illness: New Insights into Diagnosis and Management 2015 1 78 90%
Hemophagocytic syndromes 2007 211 43 88%
Identification of the best cutoff points and clinical signs specific for early recognition of macrophage activation syndrome in active systemic juvenile idiopathic arthritis 2015 1 30 83%

Address terms


Rank Address term Relevance score
(tfidf)		 Class's shr.
of term's tot.
occurrences		 Shr. of publ.
in class containing
term		 Num. of
publ. in
class
1 IMMUNODEFICIENCY HISTIOCYTOSIS PROGRAM 4 75% 0.2% 3
2 UNITE RECH DEV NORMAL PATHOL SYST IMMUNITAIRE 4 41% 0.4% 7
3 BONE MARROW TRANSPLANTAT IMMUNE DEFICIENCY 3 19% 0.8% 14
4 BONE MARROW TRANSPLANT IMMUNE DEFICIENCY 2 25% 0.3% 6
5 ABT KNOCHENMARKTRANSPLANTAT 1 50% 0.1% 2
6 IST RICOVERO CURA CARATTERE SCI S MATTEO 1 50% 0.1% 2
7 ONCO EMATOL PEDIAT 1 100% 0.1% 2
8 PAEDIAT IHOBA 1 100% 0.1% 2
9 ZENTRUM FRAUENHEILKUNDE KINDER JUGENDMED 1 100% 0.1% 2
10 ETUD DEFICITS IMMUNITAI 1 15% 0.5% 8

Related classes at same level (level 1)


Rank Relatedness score Related classes
1 0.0000149069 ADULT ONSET STILLS DISEASE//ADULT STILLS DISEASE//STILLS DISEASE
2 0.0000123547 SUBCUTANEOUS PANNICULITIS LIKE T CELL LYMPHOMA//HEPATOSPLENIC GAMMA DELTA T CELL LYMPHOMA//WEBER CHRISTIAN DISEASE
3 0.0000119398 XLP//2B4//X LINKED LYMPHOPROLIFERATIVE DISEASE
4 0.0000111177 FOLLICULAR DENDRITIC CELL SARCOMA//INTERDIGITATING DENDRITIC CELL SARCOMA//HISTIOCYTIC SARCOMA
5 0.0000077830 MYOSIN VA//RAB27A//GRISCELLI SYNDROME
6 0.0000067631 EXTRANODAL NK T CELL LYMPHOMA//NK T CELL LYMPHOMA//NASAL LYMPHOMA
7 0.0000055303 HERMANSKY PUDLAK SYNDROME//CHEDIAK HIGASHI SYNDROME//LYST
8 0.0000046251 INTRAVASCULAR LYMPHOMA//INTRAVASCULAR LYMPHOMATOSIS//ANGIOTROPIC LYMPHOMA
9 0.0000041947 GRANZYME B//GRANZYME//PERFORIN
10 0.0000040099 INFECTIOUS MONONUCLEOSIS//MONONUCLEOSIS//ACUTE EBV INFECTION