Class information for:
Level 1: TRIPLE A SYNDROME//ALACRIMA//ALLGROVE SYNDROME

Basic class information

ID Publications Average number
of references
Avg. shr. active
ref. in WoS
24759 252 24.0 74%



Bar chart of Publication_year

Last years might be incomplete

Classes in level above (level 2)



ID, lev.
above
Publications Label for level above
2292 4139 MELANOCORTIN//MELANOCORTIN RECEPTOR//MELANOCORTIN RECEPTORS

Terms with highest relevance score



Rank Term Type of term Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
1 TRIPLE A SYNDROME Author keyword 120 92% 19% 47
2 ALACRIMA Author keyword 52 80% 13% 32
3 ALLGROVE SYNDROME Author keyword 44 88% 8% 21
4 AAAS GENE Author keyword 23 100% 4% 10
5 FAMILIAL GLUCOCORTICOID DEFICIENCY Author keyword 17 72% 5% 13
6 ALACRIMIA Author keyword 15 88% 3% 7
7 ACTH RESISTANCE Author keyword 12 75% 4% 9
8 GLUCOCORTICOID DEFICIENCY Author keyword 10 57% 5% 12
9 AAAS GENE MUTATION Author keyword 8 100% 2% 5
10 ALLGROVES SYNDROME Author keyword 8 100% 2% 5

Web of Science journal categories

Author Key Words



Rank Web of Science journal category Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
LCSH search Wikipedia search
1 TRIPLE A SYNDROME 120 92% 19% 47 Search TRIPLE+A+SYNDROME Search TRIPLE+A+SYNDROME
2 ALACRIMA 52 80% 13% 32 Search ALACRIMA Search ALACRIMA
3 ALLGROVE SYNDROME 44 88% 8% 21 Search ALLGROVE+SYNDROME Search ALLGROVE+SYNDROME
4 AAAS GENE 23 100% 4% 10 Search AAAS+GENE Search AAAS+GENE
5 FAMILIAL GLUCOCORTICOID DEFICIENCY 17 72% 5% 13 Search FAMILIAL+GLUCOCORTICOID+DEFICIENCY Search FAMILIAL+GLUCOCORTICOID+DEFICIENCY
6 ALACRIMIA 15 88% 3% 7 Search ALACRIMIA Search ALACRIMIA
7 ACTH RESISTANCE 12 75% 4% 9 Search ACTH+RESISTANCE Search ACTH+RESISTANCE
8 GLUCOCORTICOID DEFICIENCY 10 57% 5% 12 Search GLUCOCORTICOID+DEFICIENCY Search GLUCOCORTICOID+DEFICIENCY
9 AAAS GENE MUTATION 8 100% 2% 5 Search AAAS+GENE+MUTATION Search AAAS+GENE+MUTATION
10 ALLGROVES SYNDROME 8 100% 2% 5 Search ALLGROVES+SYNDROME Search ALLGROVES+SYNDROME

Key Words Plus



Rank Web of Science journal category Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
1 ALLGROVE SYNDROME 103 93% 15% 39
2 ALACRIMA 90 80% 22% 56
3 FAMILIAL GLUCOCORTICOID DEFICIENCY 45 54% 23% 59
4 AAAS GENE 38 93% 6% 14
5 A SYNDROME 34 59% 15% 38
6 TRIPLE A SYNDROME 28 48% 17% 43
7 SELECTIVE ACTH INSENSITIVITY 24 91% 4% 10
8 ACTH INSENSITIVITY 23 86% 5% 12
9 WD REPEAT PROTEIN 20 28% 25% 62
10 ADRENOCORTICOTROPIN RECEPTOR GENE 15 63% 6% 15

Journals

Reviews



Title Publ. year Cit. Active
references
% act. ref.
to same field
Familial glucocorticoid deficiency: New genes and mechanisms 2013 7 26 54%
Adult or late-onset triple A syndrome Case report and literature review 2010 7 16 81%
Inherited ACTH insensitivity illuminates the mechanisms of ACTH action 2005 34 44 45%
Adrenocorticotropin insensitivity syndromes 1998 109 86 49%
Familial glucocorticoid deficiency: Advances in the molecular understanding of ACTH action 2008 19 53 51%
A novel presentation of familial glucocorticoid deficiency (FGD) and current literature review 2004 9 28 89%
Oxidative stress and adrenocortical insufficiency 2014 3 79 24%
The Molecular Basis of Adrenocorticotrophin Resistance Syndrome 2009 1 89 66%
Familial glucocorticoid deficiency: One syndrome, but more than one gene 1997 12 14 64%
The nuclear pore complex: disease associations and functional correlations 2004 37 62 24%

Address terms



Rank Address term Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ.
in class
1 WILLIAM HARVEY ENDOCRINOL 2 67% 0.8% 2
2 ENDOCRINOL MOTHER CHILD HLTH CARE 1 50% 0.4% 1
3 INRA INSERM U418 1 50% 0.4% 1
4 INRA UA953 1 50% 0.4% 1
5 PAEDIAT KANTRIDA 1 50% 0.4% 1
6 PEDIAT KANTRIDA 1 50% 0.4% 1
7 SERV CHIRURG PEDIAT B 1 22% 0.8% 2
8 DIGEST DIS NUTR NIH 0 33% 0.4% 1
9 BOALI HOSP 0 25% 0.4% 1
10 NEUROPED 0 25% 0.4% 1

Related classes at same level (level 1)



Rank Relatedness score Related classes
1 0.0000183912 MELANOCORTIN//MELANOCORTIN 4 RECEPTOR//MELANOCORTIN RECEPTOR
2 0.0000171143 ACHALASIA//HELLER MYOTOMY//PERORAL ENDOSCOPIC MYOTOMY
3 0.0000117047 ADRENAL HYPOPLASIA CONGENITA//DAX 1//STEROIDOGENIC FACTOR 1
4 0.0000073155 TRANSHYDROGENASE//NICOTINAMIDE NUCLEOTIDE//NICOTINAMIDE NUCLEOTIDE TRANSHYDROGENASE
5 0.0000061340 ALDOSTERONE BIOSYNTHESIS//ALDOSTERONE SYNTHASE DEFICIENCY//ALDOSTERONE SYNTHESIS
6 0.0000055962 SEPTO OPTIC DYSPLASIA//SEPTUM PELLUCIDUM//OPTIC NERVE HYPOPLASIA
7 0.0000054686 ACTH INDEPENDENT MACRONODULAR ADRENAL HYPERPLASIA//AIMAH//ENDOCRINE PATHOPHYSIOL
8 0.0000053936 STEROIDOGENIC ACUTE REGULATORY PROTEIN//STARD6//STEROIDOGENIC ACUTE REGULATORY PROTEIN STAR
9 0.0000052154 ADRENAL INSUFFICIENCY//RELATIVE ADRENAL INSUFFICIENCY//LOW DOSE ACTH TEST
10 0.0000044249 LACRIMAL GLAND//HUMAN LACRIMAL GLAND//AUTOIMMUNE DACRYOADENITIS