Class information for:
Level 1: FARBER DISEASE//ASAH1//FARBER LIPOGRANULOMATOSIS

Basic class information
ID Publications Average number
of references		 Avg. shr. active
ref. in WoS
24427 261 26.6 44%


Bar chart of Publication_year

Last years might be incomplete

Classes in level above (level 2)


ID, lev.
above		 Publications Label for level above
330 17366 FABRY DISEASE//GAUCHER DISEASE//MUCOPOLYSACCHARIDOSES

Terms with highest relevance score


Rank Term Type of term Relevance score
(tfidf)		 Class's shr.
of term's tot.
occurrences		 Shr. of publ.
in class containing
term		 Num. of
publ. in
class
1 FARBER DISEASE Author keyword 16 60% 7% 18
2 ASAH1 Author keyword 6 80% 2% 4
3 FARBER LIPOGRANULOMATOSIS Author keyword 3 100% 1% 3
4 FARBERS DISEASE Author keyword 3 100% 1% 3
5 ACID CERAMIDASE Author keyword 3 22% 4% 11
6 FLUORESCENT FATTY ACIDS Author keyword 2 67% 1% 2
7 FARBERS LIPOGRANULOMATOSIS Author keyword 1 100% 1% 2
8 FLUORESCENT SULFATIDE Author keyword 1 100% 1% 2
9 SULFATIDE METABOLISM Author keyword 1 50% 1% 2
10 LIPOGRANULOMATOSIS Author keyword 1 22% 2% 4

Web of Science journal categories

Author Key Words


Rank Web of Science journal category Relevance score
(tfidf)		 Class's shr.
of term's tot.
occurrences		 Shr. of publ.
in class containing
term		 Num. of
publ. in
class		 LCSH search Wikipedia search
1 FARBER DISEASE 16 60% 7% 18 Search FARBER+DISEASE Search FARBER+DISEASE
2 ASAH1 6 80% 2% 4 Search ASAH1 Search ASAH1
3 FARBER LIPOGRANULOMATOSIS 3 100% 1% 3 Search FARBER+LIPOGRANULOMATOSIS Search FARBER+LIPOGRANULOMATOSIS
4 FARBERS DISEASE 3 100% 1% 3 Search FARBERS+DISEASE Search FARBERS+DISEASE
5 ACID CERAMIDASE 3 22% 4% 11 Search ACID+CERAMIDASE Search ACID+CERAMIDASE
6 FLUORESCENT FATTY ACIDS 2 67% 1% 2 Search FLUORESCENT+FATTY+ACIDS Search FLUORESCENT+FATTY+ACIDS
7 FARBERS LIPOGRANULOMATOSIS 1 100% 1% 2 Search FARBERS+LIPOGRANULOMATOSIS Search FARBERS+LIPOGRANULOMATOSIS
8 FLUORESCENT SULFATIDE 1 100% 1% 2 Search FLUORESCENT+SULFATIDE Search FLUORESCENT+SULFATIDE
9 SULFATIDE METABOLISM 1 50% 1% 2 Search SULFATIDE+METABOLISM Search SULFATIDE+METABOLISM
10 LIPOGRANULOMATOSIS 1 22% 2% 4 Search LIPOGRANULOMATOSIS Search LIPOGRANULOMATOSIS

Key Words Plus


Rank Web of Science journal category Relevance score
(tfidf)		 Class's shr.
of term's tot.
occurrences		 Shr. of publ.
in class containing
term		 Num. of
publ. in
class
1 LIPOGRANULOMATOSIS 12 86% 2% 6
2 ALKALINE CERAMIDASES 5 63% 2% 5
3 CONTAINING FATTY ACID 3 100% 1% 3
4 L IDURONIDASE ACTIVITY 3 60% 1% 3
5 DISSEMINATED LIPOGRANULOMATOSIS 1 100% 1% 2
6 LYSOSOMAL ACID CERAMIDASE 1 100% 1% 2
7 CEREBROSIDE SULFATE 1 11% 4% 10
8 FARBER DISEASE 1 16% 2% 6
9 ACID CERAMIDASE 1 11% 3% 7
10 ACID CERAMIDASE GENE 1 50% 0% 1

Journals

Reviews


Title Publ. year Cit. Active references % act. ref.
to same field
SPHINGOMYELINASES AND NIEMANN-PICK DISEASE 1986 35 67 54%
Synthesis of fluorescent substrates and their application to study of sphingolipid metabolism in vitro and in intact cells 2000 4 19 63%
Pyrene-labeled lipids as tools in membrane biophysics and cell biology 2002 74 169 9%
The molecular medicine of acid ceramidase 2015 0 39 23%
Fluorescence-based selection of gene-corrected hematopoietic stem and progenitor cells based on acid sphingomyelinase expression 2000 0 10 30%
ALPHA-GALACTOSIDASES AND ALPHA-N-ACETYLGALACTOSAMINIDASES - MOLECULAR-BASES OF FABRY DISEASE 1984 2 8 25%

Address terms


Rank Address term Relevance score
(tfidf)		 Class's shr.
of term's tot.
occurrences		 Shr. of publ.
in class containing
term		 Num. of
publ.
in class
1 GENOM TRANSCRIPT IL 1 50% 0.4% 1
2 PEDIAT PEDIAT HEPATOL 1 50% 0.4% 1
3 RECH CANC TOULOUSE 1 29% 0.8% 2
4 INSERM UMR1037 1 18% 1.1% 3
5 BIOMED BICETRE 0 33% 0.4% 1
6 HADASSAH MED MOLEC GENET 0 25% 0.4% 1
7 LOUIS BUGNARDINSERM 0 25% 0.4% 1
8 POST PROGRAM BIOL SCI BIOCHEM 0 10% 0.8% 2
9 BIOCHIM METABOL 0 17% 0.4% 1
10 EQUIPE 14 0 17% 0.4% 1

Related classes at same level (level 1)


Rank Relatedness score Related classes
1 0.0000232784 NIEMANN PICK DISEASE TYPE C//NIEMANN PICK TYPE C//NIEMANN PICK DISEASE
2 0.0000194997 CERAMIDE//SPHINGOMYELINASE//CERAMIDE 1 PHOSPHATE
3 0.0000163362 PROSAPOSIN//SPHINGOLIPID ACTIVATOR PROTEIN//SAPOSIN B
4 0.0000158811 GLOBOID CELL LEUKODYSTROPHY//KRABBE DISEASE//PSYCHOSINE
5 0.0000145719 CHOLESTERYL ESTER STORAGE DISEASE//LYSOSOMAL ACID LIPASE//WOLMAN DISEASE
6 0.0000105285 METACHROMATIC LEUKODYSTROPHY//ARYLSULFATASE A//MULTIPLE SULFATASE DEFICIENCY
7 0.0000101152 GM2 GANGLIOSIDOSIS//SANDHOFF DISEASE//TAY SACHS DISEASE
8 0.0000100987 MEROCYANINE 540//BIOMED SPECT//MEROCYANINE 540 MC540
9 0.0000095053 POLYVALENT ANTIBODY//FOOD ADDIT EVALUAT//ALPHA BETA GLOBULINS
10 0.0000079821 JUVENILE HYALINE FIBROMATOSIS//INFANTILE SYSTEMIC HYALINOSIS//SYSTEMIC HYALINOSIS