Class information for:
Level 1: HIRAYAMA DISEASE//BROWN VIALETTO VAN LAERE SYNDROME//MONOMELIC AMYOTROPHY

Basic class information
ID Publications Average number
of references		 Avg. shr. active
ref. in WoS
21632 354 21.0 62%


Bar chart of Publication_year

Last years might be incomplete

Classes in level above (level 2)


ID, lev.
above		 Publications Label for level above
799 11424 AMYOTROPHIC LATERAL SCLEROSIS//SPINAL MUSCULAR ATROPHY//MOTOR NEURON DISEASE

Terms with highest relevance score


Rank Term Type of term Relevance score
(tfidf)		 Class's shr.
of term's tot.
occurrences		 Shr. of publ.
in class containing
term		 Num. of
publ. in
class
1 HIRAYAMA DISEASE Author keyword 108 87% 15% 53
2 BROWN VIALETTO VAN LAERE SYNDROME Author keyword 51 91% 6% 21
3 MONOMELIC AMYOTROPHY Author keyword 44 85% 6% 23
4 CERVICAL FLEXION MYELOPATHY Author keyword 26 87% 4% 13
5 FLEXION MYELOPATHY Author keyword 24 91% 3% 10
6 HIRAYAMAS DISEASE Author keyword 21 90% 3% 9
7 ATOPIC MYELITIS Author keyword 18 89% 2% 8
8 PONTOBULBAR PALSY Author keyword 14 100% 2% 7
9 HOPKINS SYNDROME Author keyword 11 78% 2% 7
10 MADRAS MOTOR NEURON DISEASE Author keyword 9 83% 1% 5

Web of Science journal categories

Author Key Words


Rank Web of Science journal category Relevance score
(tfidf)		 Class's shr.
of term's tot.
occurrences		 Shr. of publ.
in class containing
term		 Num. of
publ. in
class		 LCSH search Wikipedia search
1 HIRAYAMA DISEASE 108 87% 15% 53 Search HIRAYAMA+DISEASE Search HIRAYAMA+DISEASE
2 BROWN VIALETTO VAN LAERE SYNDROME 51 91% 6% 21 Search BROWN+VIALETTO+VAN+LAERE+SYNDROME Search BROWN+VIALETTO+VAN+LAERE+SYNDROME
3 MONOMELIC AMYOTROPHY 44 85% 6% 23 Search MONOMELIC+AMYOTROPHY Search MONOMELIC+AMYOTROPHY
4 CERVICAL FLEXION MYELOPATHY 26 87% 4% 13 Search CERVICAL+FLEXION+MYELOPATHY Search CERVICAL+FLEXION+MYELOPATHY
5 FLEXION MYELOPATHY 24 91% 3% 10 Search FLEXION+MYELOPATHY Search FLEXION+MYELOPATHY
6 HIRAYAMAS DISEASE 21 90% 3% 9 Search HIRAYAMAS+DISEASE Search HIRAYAMAS+DISEASE
7 ATOPIC MYELITIS 18 89% 2% 8 Search ATOPIC+MYELITIS Search ATOPIC+MYELITIS
8 PONTOBULBAR PALSY 14 100% 2% 7 Search PONTOBULBAR+PALSY Search PONTOBULBAR+PALSY
9 HOPKINS SYNDROME 11 78% 2% 7 Search HOPKINS+SYNDROME Search HOPKINS+SYNDROME
10 MADRAS MOTOR NEURON DISEASE 9 83% 1% 5 Search MADRAS+MOTOR+NEURON+DISEASE Search MADRAS+MOTOR+NEURON+DISEASE

Key Words Plus


Rank Web of Science journal category Relevance score
(tfidf)		 Class's shr.
of term's tot.
occurrences		 Shr. of publ.
in class containing
term		 Num. of
publ. in
class
1 JUVENILE MUSCULAR ATROPHY 103 78% 19% 68
2 DISTAL UPPER EXTREMITY 100 76% 20% 71
3 VANLAERE SYNDROME 69 93% 7% 26
4 PONTOBULBAR PALSY 44 100% 5% 16
5 MONOMELIC AMYOTROPHY 28 64% 8% 27
6 HIRAYAMA DISEASE 27 78% 5% 18
7 HYPERIGEEMIA 18 89% 2% 8
8 HOPKINS SYNDROME 15 88% 2% 7
9 BENIGN FOCAL AMYOTROPHY 14 100% 2% 7
10 CERVICAL FLEXION MYELOPATHY 11 100% 2% 6

Journals

Reviews


Title Publ. year Cit. Active
references		 % act. ref.
to same field
CLIPPERS: chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids. Review of an increasingly recognized entity within the spectrum of inflammatory central nervous system disorders 2014 7 25 44%
The Brown-Vialetto-Van Laere and Fazio Londe syndrome revisited: natural history, genetics, treatment and future perspectives 2012 21 25 88%
Brown-Vialetto-Van Laere syndrome 2008 24 26 88%
Juvenile muscular atrophy of distal upper extremity (Hirayama disease) 2000 61 18 100%
Hirayama disease in Germany 2011 3 43 100%
Brown-Vialetto-Van Laere syndrome: A rare syndrome in otology - case report and literature review 2005 6 5 100%
Atopy and neural damage 2002 10 20 60%
Brown-Vialetto-Van Laere syndrome: Case report and literature review 2000 16 8 100%
Hirayama disease 2015 0 14 93%
Recurrent Hopkin's syndrome: A case report and review of the literature 2010 1 11 100%

Address terms


Rank Address term Relevance score
(tfidf)		 Class's shr.
of term's tot.
occurrences		 Shr. of publ.
in class containing
term		 Num. of
publ.
in class
1 COMMAND HOSP 1 33% 0.6% 2
2 ASSOCIE INSERM UMR S 910 1 50% 0.3% 1
3 AZIENDA OSPEDAL UNIV 1 50% 0.3% 1
4 CHILDRENS HOSP REYKJAVIK 1 50% 0.3% 1
5 CLIN NEUROL BEHAV SCI 1 50% 0.3% 1
6 FLUMINENSE MED 1 50% 0.3% 1
7 GRP PNEUMOL PEDIAT 1 50% 0.3% 1
8 NEUROSCI BLOCK 1 50% 0.3% 1
9 NEUROWISSEN MED INM3 1 50% 0.3% 1
10 CHILDREN NEUROPSYCHIAT OPERAT UNIT 0 33% 0.3% 1

Related classes at same level (level 1)


Rank Relatedness score Related classes
1 0.0000088795 RIGID SPINE SYNDROME//RIGID SPINE//EMERINOPATHY
2 0.0000081858 SPINAL AND BULBAR MUSCULAR ATROPHY//KENNEDYS DISEASE//KENNEDY DISEASE
3 0.0000073475 RIBOFLAVIN CARRIER PROTEIN//FAD SYNTHETASE//RIBOFLAVIN DEFICIENCY
4 0.0000060222 PRIMARY LATERAL SCLEROSIS//BUNINA BODY//MOTOR NEURON DISEASE
5 0.0000055612 AMYOTROPHIC LATERAL SCLEROSIS//AMYOTROPHIC LATERAL SCLEROSIS AND FRONTOTEMPORAL DEGENERATION//MOTOR NEURON DISEASE
6 0.0000051400 MULTIFOCAL MOTOR NEUROPATHY//CHRONIC INFLAMMATORY DEMYELINATING POLYNEUROPATHY//CIDP
7 0.0000050766 POST POLIO SYNDROME//POSTPOLIOMYELITIS SYNDROME//POLIOMYELITIS
8 0.0000049179 NEUROMYELITIS OPTICA//NMO IGG//ANTI AQUAPORIN 4 ANTIBODY
9 0.0000048048 SPINAL MUSCULAR ATROPHY//SURVIVAL MOTOR NEURON//SMN2
10 0.0000047469 LAMINOPLASTY//OSSIFICATION OF THE POSTERIOR LONGITUDINAL LIGAMENT//CERVICAL SPONDYLOTIC MYELOPATHY