Class information for:
Level 1: GYRATE ATROPHY//GYRATE ATROPHY OF THE CHOROID AND RETINA//ORNITHINE AMINOTRANSFERASE

Basic class information

ID Publications Average number
of references
Avg. shr. active
ref. in WoS
21359 363 26.8 42%



Bar chart of Publication_year

Last years might be incomplete

Classes in level above (level 2)



ID, lev.
above
Publications Label for level above
1850 5585 ARGINASE//ORNITHINE TRANSCARBAMYLASE DEFICIENCY//SLC25A13

Terms with highest relevance score



Rank Term Type of term Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
1 GYRATE ATROPHY Author keyword 19 63% 5% 19
2 GYRATE ATROPHY OF THE CHOROID AND RETINA Author keyword 9 83% 1% 5
3 ORNITHINE AMINOTRANSFERASE Author keyword 6 29% 5% 17
4 HYPERORNITHINEMIA Author keyword 4 46% 2% 6
5 5 FLUOROMETHYLORNITHINE Author keyword 3 60% 1% 3
6 HYPERORNITHINAEMIA Author keyword 2 67% 1% 2
7 ORNITHINE DELTA AMINOTRANSFERASE Author keyword 2 29% 1% 5
8 EQUIPE MIXTE RECH 0322 Address 1 50% 0% 1
9 INSERMU499 Address 1 50% 0% 1
10 ISOLATED NEPHRON SEGMENTS Author keyword 1 50% 0% 1

Web of Science journal categories

Author Key Words



Rank Web of Science journal category Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
LCSH search Wikipedia search
1 GYRATE ATROPHY 19 63% 5% 19 Search GYRATE+ATROPHY Search GYRATE+ATROPHY
2 GYRATE ATROPHY OF THE CHOROID AND RETINA 9 83% 1% 5 Search GYRATE+ATROPHY+OF+THE+CHOROID+AND+RETINA Search GYRATE+ATROPHY+OF+THE+CHOROID+AND+RETINA
3 ORNITHINE AMINOTRANSFERASE 6 29% 5% 17 Search ORNITHINE+AMINOTRANSFERASE Search ORNITHINE+AMINOTRANSFERASE
4 HYPERORNITHINEMIA 4 46% 2% 6 Search HYPERORNITHINEMIA Search HYPERORNITHINEMIA
5 5 FLUOROMETHYLORNITHINE 3 60% 1% 3 Search 5+FLUOROMETHYLORNITHINE Search 5+FLUOROMETHYLORNITHINE
6 HYPERORNITHINAEMIA 2 67% 1% 2 Search HYPERORNITHINAEMIA Search HYPERORNITHINAEMIA
7 ORNITHINE DELTA AMINOTRANSFERASE 2 29% 1% 5 Search ORNITHINE+DELTA+AMINOTRANSFERASE Search ORNITHINE+DELTA+AMINOTRANSFERASE
8 ISOLATED NEPHRON SEGMENTS 1 50% 0% 1 Search ISOLATED+NEPHRON+SEGMENTS Search ISOLATED+NEPHRON+SEGMENTS
9 MUSCULAR TONE 1 50% 0% 1 Search MUSCULAR+TONE Search MUSCULAR+TONE
10 ORNITHINE SUPPLEMENTATION 1 50% 0% 1 Search ORNITHINE+SUPPLEMENTATION Search ORNITHINE+SUPPLEMENTATION

Key Words Plus



Rank Web of Science journal category Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
1 DELTA AMINOTRANSFERASE 23 79% 4% 15
2 HYPERORNITHINEMIA 13 47% 6% 21
3 GYRATE ATROPHY 12 28% 10% 35
4 KETOACID TRANSAMINASE DEFICIENCY 4 75% 1% 3
5 5 FLUOROMETHYLORNITHINE 3 57% 1% 4
6 ENDOGENOUS ORNITHINE 3 100% 1% 3
7 L ORNITHINE 2 OXOACID AMINOTRANSFERASE 3 100% 1% 3
8 OAT LOCUS 3 100% 1% 3
9 ORNITHINE AMINOTRANSFERASE DEFICIENCY 3 100% 1% 3
10 PLASMA ORNITHINE 3 100% 1% 3

Journals

Reviews



Title Publ. year Cit. Active
references
% act. ref.
to same field
Retinal risks of high-dose ornithine supplements: a review 2011 4 68 49%
Nutritional Therapies for Ocular Disorders: Part Three 2008 2 31 39%
ENDOGENOUS ORNITHINE IN SEARCH FOR CNS FUNCTIONS AND THERAPEUTIC APPLICATIONS 1993 6 85 31%
Ornithine aminotransferase as a therapeutic target in hyperammonemias 1997 2 86 28%
Inhibition of ornithine aminotransferase: A new target for therapeutic intervention 1996 0 52 37%
GLUTAMATE-ORNITHINE TRANSAMINASES 1985 1 1 100%
METABOLIC TAPETORETINAL DEGENERATIONS 1982 23 22 73%
METABOLIC PIGMENTARY RETINOPATHIES - DIAGNOSIS AND THERAPEUTIC ATTEMPTS 1992 14 20 10%
ENZYMES OF ARGININE METABOLISM IN THE LIZARD CALOTES VERSICOLOR 1982 0 2 100%
ACQUIRED DEFICIENCIES OF HUMAN COLOR-VISION 1993 0 50 4%

Address terms



Rank Address term Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ.
in class
1 EQUIPE MIXTE RECH 0322 1 50% 0.3% 1
2 INSERMU499 1 50% 0.3% 1
3 REFERENCE METAB DISORDERS 1 50% 0.3% 1
4 URA 219 1 50% 0.3% 1
5 PADIAT 1 0 33% 0.3% 1
6 PATHOL VASC ENDOCRINOL RENALE 0 33% 0.3% 1
7 BIOL NUTR EA2498 0 25% 0.3% 1
8 PEDIAT NUTR METAB UNIT 0 25% 0.3% 1
9 RADIOL ASSOCIATES SACRAMENTO 0 25% 0.3% 1
10 AMINO ACID DISORDERS 0 20% 0.3% 1

Related classes at same level (level 1)



Rank Relatedness score Related classes
1 0.0000208049 DYE LINKED L PROLINE DEHYDROGENASE//PUTA//N ACETYLTRANSFERASE MPR1
2 0.0000159297 HYPERPROLINEMIA//HYPERPROLINEMIA TYPE II//SUPERIOR MESENTERIC FLOW
3 0.0000105204 UVEAL INFLAMMATION//IRIS CILIARY COMPLEX//OCULAR TISSUE
4 0.0000102163 4 AMINOBUTYRATE AMINOTRANSFERASE//GAMMA AMINOBUTYRIC ACID AMINOTRANSFERASE//GABA AT
5 0.0000092497 CHOROIDEREMIA//POU3F4//DFN3
6 0.0000086896 HINOSAN//ORGANOPHOSPHORUS FUNGICIDE//WEATTABILITY
7 0.0000085039 ARGINASE//NOR NOHA//ARGINASE II
8 0.0000074658 ARCAINE//HYPOPERFUSION REPERFUSION//ALPHA DIFLUOROMETHYLORNITHINE
9 0.0000073273 ASPARTATE AMINOTRANSFERASE//AROMATIC AMINO ACID AMINOTRANSFERASE//PYRIDOXAL 5 PHOSPHATE
10 0.0000066003 PIGMENTED PARAVENOUS RETINOCHOROIDAL ATROPHY//ATYPICAL RETINITIS PIGMENTOSA//PARAVENOUS