Class information for:
Level 1: NONKETOTIC HYPERGLYCINEMIA//NON KETOTIC HYPERGLYCINEMIA//GLYCINE N ACYLTRANSFERASE

Basic class information

ID Publications Average number
of references
Avg. shr. active
ref. in WoS
20747 386 25.7 57%



Bar chart of Publication_year

Last years might be incomplete

Classes in level above (level 2)



ID, lev.
above
Publications Label for level above
2279 4195 LIPOYL DOMAIN//PYRUVATE DEHYDROGENASE COMPLEX//NONKETOTIC HYPERGLYCINEMIA

Terms with highest relevance score



Rank Term Type of term Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
1 NONKETOTIC HYPERGLYCINEMIA Author keyword 65 84% 9% 36
2 NON KETOTIC HYPERGLYCINEMIA Author keyword 19 74% 4% 14
3 GLYCINE N ACYLTRANSFERASE Author keyword 18 89% 2% 8
4 MEDIUM CHAIN ACYL COA SYNTHETASE Author keyword 15 88% 2% 7
5 NKH Author keyword 14 100% 2% 7
6 GLYCINE CLEAVAGE SYSTEM Author keyword 12 56% 4% 15
7 GLDC Author keyword 9 83% 1% 5
8 T PROTEIN Author keyword 9 67% 2% 8
9 GLYCINE ENCEPHALOPATHY Author keyword 8 62% 2% 8
10 AMINO ACID CONJUGATION Author keyword 5 60% 2% 6

Web of Science journal categories

Author Key Words



Rank Web of Science journal category Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
LCSH search Wikipedia search
1 NONKETOTIC HYPERGLYCINEMIA 65 84% 9% 36 Search NONKETOTIC+HYPERGLYCINEMIA Search NONKETOTIC+HYPERGLYCINEMIA
2 NON KETOTIC HYPERGLYCINEMIA 19 74% 4% 14 Search NON+KETOTIC+HYPERGLYCINEMIA Search NON+KETOTIC+HYPERGLYCINEMIA
3 GLYCINE N ACYLTRANSFERASE 18 89% 2% 8 Search GLYCINE+N+ACYLTRANSFERASE Search GLYCINE+N+ACYLTRANSFERASE
4 MEDIUM CHAIN ACYL COA SYNTHETASE 15 88% 2% 7 Search MEDIUM+CHAIN+ACYL+COA+SYNTHETASE Search MEDIUM+CHAIN+ACYL+COA+SYNTHETASE
5 NKH 14 100% 2% 7 Search NKH Search NKH
6 GLYCINE CLEAVAGE SYSTEM 12 56% 4% 15 Search GLYCINE+CLEAVAGE+SYSTEM Search GLYCINE+CLEAVAGE+SYSTEM
7 GLDC 9 83% 1% 5 Search GLDC Search GLDC
8 T PROTEIN 9 67% 2% 8 Search T+PROTEIN Search T+PROTEIN
9 GLYCINE ENCEPHALOPATHY 8 62% 2% 8 Search GLYCINE+ENCEPHALOPATHY Search GLYCINE+ENCEPHALOPATHY
10 AMINO ACID CONJUGATION 5 60% 2% 6 Search AMINO+ACID+CONJUGATION Search AMINO+ACID+CONJUGATION

Key Words Plus



Rank Web of Science journal category Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
1 NON KETOTIC HYPERGLYCINEMIA 56 89% 6% 25
2 T PROTEIN GENE 31 92% 3% 12
3 NONKETOTIC HYPERGLYCINEMIA 28 40% 14% 54
4 GLDC 21 90% 2% 9
5 ARALKYL COA 18 89% 2% 8
6 BOVINE LIVER MITOCHONDRIA 15 73% 3% 11
7 GLYCINE CLEAVAGE SYSTEM 11 28% 9% 34
8 STRUCTURE METABOLISM RELATIONSHIP 11 78% 2% 7
9 NKH 8 100% 1% 5
10 CLEAVAGE SYSTEM 8 29% 6% 22

Journals

Reviews



Title Publ. year Cit. Active references % act. ref.
to same field
Glycine cleavage system: reaction mechanism, physiological significance, and hyperglycinemia 2008 55 54 54%
Nonketotic hyperglycinemia (glycine encephalopathy): Laboratory diagnosis 2001 54 48 81%
Atypical variants of nonketotic hyperglycinemia 2005 27 38 89%
Pitfalls in the diagnosis of glycine encephalopathy (non-ketotic hyperglycinemia) 2002 24 72 67%
Clinical, ethical and legal considerations in the treatment of newborns with non-ketotic hyperglycinaemia 2008 6 20 90%
Amino acid conjugation: contribution to the metabolism and toxicity of xenobiotic carboxylic acids 2007 28 45 38%
Nonketotic hyperglycinemia: Pathophysiological studies 2005 4 46 91%
NONKETOTIC HYPERGLYCINEMIA - CLINICAL AND BIOCHEMICAL ASPECTS 1987 38 21 90%
The glycine deportation system and its pharmacological consequences 2012 12 110 22%
Current status of NMDA antagonist interventions in the treatment of nonketotic hyperglycinemia 1998 7 15 80%

Address terms



Rank Address term Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ.
in class
1 TOHOKU HOSP 1 40% 0.5% 2
2 CHILDRENS HOSP BOST 1 50% 0.3% 1
3 HEREDITARY METAB DIS SERV 1 50% 0.3% 1
4 MED HOWARD HUGHES MED NEUROL 1 50% 0.3% 1
5 MED HOWARD HUGHES MED PEDIAT 1 50% 0.3% 1
6 MURDOCH CHILDRENS METAB SERV 1 50% 0.3% 1
7 NEURO INTENS CARE NURSERY GRP 1 50% 0.3% 1
8 PEDIAT NEONATAL INTENS CARE MED 1 50% 0.3% 1
9 PEDIAT PHARMACOL EXPT THER EUT 1 50% 0.3% 1
10 PEDIAT PULM HYPERTENS UNIT 1 50% 0.3% 1

Related classes at same level (level 1)



Rank Relatedness score Related classes
1 0.0000246597 GLYCINE REDUCTASE//EUBACTERIUM ACIDAMINOPHILUM//SARCOSINE REDUCTASE
2 0.0000111614 LIPOYL DOMAIN//PYRUVATE DEHYDROGENASE COMPLEX//DIHYDROLIPOAMIDE DEHYDROGENASE
3 0.0000101538 SERINE BIOSYNTHESIS//PHOSPHORYLATED PATHWAY//3 PHOSPHOGLYCERATE DEHYDROGENASE
4 0.0000091137 SERINE HYDROXYMETHYLTRANSFERASE//THREONINE ALDOLASE//BIOCATALYT CHEM
5 0.0000090068 ORNITHINE TRANSCARBAMYLASE DEFICIENCY//SLC25A13//CITRIN DEFICIENCY
6 0.0000083936 METHYLMALONIC ACIDEMIA//PROPIONIC ACIDEMIA//METHYLMALONIC ACIDURIA
7 0.0000074951 PYRIDOXINE DEPENDENT EPILEPSY//PYRIDOXINE DEPENDENT SEIZURES//ALDH7A1
8 0.0000065728 THREONINE DEHYDROGENASE//SERINE DEHYDRATASE//L THREONINE DEHYDROGENASE
9 0.0000055289 GLYT1//GLYCINE TRANSPORTER//GLYT 1
10 0.0000053974 VICI SYNDROME//AGENESIS OF THE CORPUS CALLOSUM//CALLOSAL AGENESIS