Class information for: |
Basic class information |
ID | Publications | Average number of references |
Avg. shr. active ref. in WoS |
---|---|---|---|
20747 | 386 | 25.7 | 57% |
Classes in level above (level 2) |
ID, lev. above |
Publications | Label for level above |
---|---|---|
2279 | 4195 | LIPOYL DOMAIN//PYRUVATE DEHYDROGENASE COMPLEX//NONKETOTIC HYPERGLYCINEMIA |
Terms with highest relevance score |
Rank | Term | Type of term | Relevance score (tfidf) |
Class's shr. of term's tot. occurrences |
Shr. of publ. in class containing term |
Num. of publ. in class |
---|---|---|---|---|---|---|
1 | NONKETOTIC HYPERGLYCINEMIA | Author keyword | 65 | 84% | 9% | 36 |
2 | NON KETOTIC HYPERGLYCINEMIA | Author keyword | 19 | 74% | 4% | 14 |
3 | GLYCINE N ACYLTRANSFERASE | Author keyword | 18 | 89% | 2% | 8 |
4 | MEDIUM CHAIN ACYL COA SYNTHETASE | Author keyword | 15 | 88% | 2% | 7 |
5 | NKH | Author keyword | 14 | 100% | 2% | 7 |
6 | GLYCINE CLEAVAGE SYSTEM | Author keyword | 12 | 56% | 4% | 15 |
7 | GLDC | Author keyword | 9 | 83% | 1% | 5 |
8 | T PROTEIN | Author keyword | 9 | 67% | 2% | 8 |
9 | GLYCINE ENCEPHALOPATHY | Author keyword | 8 | 62% | 2% | 8 |
10 | AMINO ACID CONJUGATION | Author keyword | 5 | 60% | 2% | 6 |
Web of Science journal categories |
Author Key Words |
Rank | Web of Science journal category | Relevance score (tfidf) |
Class's shr. of term's tot. occurrences |
Shr. of publ. in class containing term |
Num. of publ. in class |
LCSH search | Wikipedia search |
---|---|---|---|---|---|---|---|
1 | NONKETOTIC HYPERGLYCINEMIA | 65 | 84% | 9% | 36 | Search NONKETOTIC+HYPERGLYCINEMIA | Search NONKETOTIC+HYPERGLYCINEMIA |
2 | NON KETOTIC HYPERGLYCINEMIA | 19 | 74% | 4% | 14 | Search NON+KETOTIC+HYPERGLYCINEMIA | Search NON+KETOTIC+HYPERGLYCINEMIA |
3 | GLYCINE N ACYLTRANSFERASE | 18 | 89% | 2% | 8 | Search GLYCINE+N+ACYLTRANSFERASE | Search GLYCINE+N+ACYLTRANSFERASE |
4 | MEDIUM CHAIN ACYL COA SYNTHETASE | 15 | 88% | 2% | 7 | Search MEDIUM+CHAIN+ACYL+COA+SYNTHETASE | Search MEDIUM+CHAIN+ACYL+COA+SYNTHETASE |
5 | NKH | 14 | 100% | 2% | 7 | Search NKH | Search NKH |
6 | GLYCINE CLEAVAGE SYSTEM | 12 | 56% | 4% | 15 | Search GLYCINE+CLEAVAGE+SYSTEM | Search GLYCINE+CLEAVAGE+SYSTEM |
7 | GLDC | 9 | 83% | 1% | 5 | Search GLDC | Search GLDC |
8 | T PROTEIN | 9 | 67% | 2% | 8 | Search T+PROTEIN | Search T+PROTEIN |
9 | GLYCINE ENCEPHALOPATHY | 8 | 62% | 2% | 8 | Search GLYCINE+ENCEPHALOPATHY | Search GLYCINE+ENCEPHALOPATHY |
10 | AMINO ACID CONJUGATION | 5 | 60% | 2% | 6 | Search AMINO+ACID+CONJUGATION | Search AMINO+ACID+CONJUGATION |
Key Words Plus |
Rank | Web of Science journal category | Relevance score (tfidf) |
Class's shr. of term's tot. occurrences |
Shr. of publ. in class containing term |
Num. of publ. in class |
---|---|---|---|---|---|
1 | NON KETOTIC HYPERGLYCINEMIA | 56 | 89% | 6% | 25 |
2 | T PROTEIN GENE | 31 | 92% | 3% | 12 |
3 | NONKETOTIC HYPERGLYCINEMIA | 28 | 40% | 14% | 54 |
4 | GLDC | 21 | 90% | 2% | 9 |
5 | ARALKYL COA | 18 | 89% | 2% | 8 |
6 | BOVINE LIVER MITOCHONDRIA | 15 | 73% | 3% | 11 |
7 | GLYCINE CLEAVAGE SYSTEM | 11 | 28% | 9% | 34 |
8 | STRUCTURE METABOLISM RELATIONSHIP | 11 | 78% | 2% | 7 |
9 | NKH | 8 | 100% | 1% | 5 |
10 | CLEAVAGE SYSTEM | 8 | 29% | 6% | 22 |
Journals |
Reviews |
Title | Publ. year | Cit. | Active references | % act. ref. to same field |
---|---|---|---|---|
Glycine cleavage system: reaction mechanism, physiological significance, and hyperglycinemia | 2008 | 55 | 54 | 54% |
Nonketotic hyperglycinemia (glycine encephalopathy): Laboratory diagnosis | 2001 | 54 | 48 | 81% |
Atypical variants of nonketotic hyperglycinemia | 2005 | 27 | 38 | 89% |
Pitfalls in the diagnosis of glycine encephalopathy (non-ketotic hyperglycinemia) | 2002 | 24 | 72 | 67% |
Clinical, ethical and legal considerations in the treatment of newborns with non-ketotic hyperglycinaemia | 2008 | 6 | 20 | 90% |
Amino acid conjugation: contribution to the metabolism and toxicity of xenobiotic carboxylic acids | 2007 | 28 | 45 | 38% |
Nonketotic hyperglycinemia: Pathophysiological studies | 2005 | 4 | 46 | 91% |
NONKETOTIC HYPERGLYCINEMIA - CLINICAL AND BIOCHEMICAL ASPECTS | 1987 | 38 | 21 | 90% |
The glycine deportation system and its pharmacological consequences | 2012 | 12 | 110 | 22% |
Current status of NMDA antagonist interventions in the treatment of nonketotic hyperglycinemia | 1998 | 7 | 15 | 80% |
Address terms |
Rank | Address term | Relevance score (tfidf) |
Class's shr. of term's tot. occurrences |
Shr. of publ. in class containing term |
Num. of publ. in class |
---|---|---|---|---|---|
1 | TOHOKU HOSP | 1 | 40% | 0.5% | 2 |
2 | CHILDRENS HOSP BOST | 1 | 50% | 0.3% | 1 |
3 | HEREDITARY METAB DIS SERV | 1 | 50% | 0.3% | 1 |
4 | MED HOWARD HUGHES MED NEUROL | 1 | 50% | 0.3% | 1 |
5 | MED HOWARD HUGHES MED PEDIAT | 1 | 50% | 0.3% | 1 |
6 | MURDOCH CHILDRENS METAB SERV | 1 | 50% | 0.3% | 1 |
7 | NEURO INTENS CARE NURSERY GRP | 1 | 50% | 0.3% | 1 |
8 | PEDIAT NEONATAL INTENS CARE MED | 1 | 50% | 0.3% | 1 |
9 | PEDIAT PHARMACOL EXPT THER EUT | 1 | 50% | 0.3% | 1 |
10 | PEDIAT PULM HYPERTENS UNIT | 1 | 50% | 0.3% | 1 |
Related classes at same level (level 1) |
Rank | Relatedness score | Related classes |
---|---|---|
1 | 0.0000246597 | GLYCINE REDUCTASE//EUBACTERIUM ACIDAMINOPHILUM//SARCOSINE REDUCTASE |
2 | 0.0000111614 | LIPOYL DOMAIN//PYRUVATE DEHYDROGENASE COMPLEX//DIHYDROLIPOAMIDE DEHYDROGENASE |
3 | 0.0000101538 | SERINE BIOSYNTHESIS//PHOSPHORYLATED PATHWAY//3 PHOSPHOGLYCERATE DEHYDROGENASE |
4 | 0.0000091137 | SERINE HYDROXYMETHYLTRANSFERASE//THREONINE ALDOLASE//BIOCATALYT CHEM |
5 | 0.0000090068 | ORNITHINE TRANSCARBAMYLASE DEFICIENCY//SLC25A13//CITRIN DEFICIENCY |
6 | 0.0000083936 | METHYLMALONIC ACIDEMIA//PROPIONIC ACIDEMIA//METHYLMALONIC ACIDURIA |
7 | 0.0000074951 | PYRIDOXINE DEPENDENT EPILEPSY//PYRIDOXINE DEPENDENT SEIZURES//ALDH7A1 |
8 | 0.0000065728 | THREONINE DEHYDROGENASE//SERINE DEHYDRATASE//L THREONINE DEHYDROGENASE |
9 | 0.0000055289 | GLYT1//GLYCINE TRANSPORTER//GLYT 1 |
10 | 0.0000053974 | VICI SYNDROME//AGENESIS OF THE CORPUS CALLOSUM//CALLOSAL AGENESIS |