Class information for:
Level 1: PYRIDOXINE DEPENDENT EPILEPSY//PYRIDOXINE DEPENDENT SEIZURES//ALDH7A1

Basic class information

ID Publications Average number
of references
Avg. shr. active
ref. in WoS
20148 411 26.3 57%



Bar chart of Publication_year

Last years might be incomplete

Classes in level above (level 2)



ID, lev.
above
Publications Label for level above
1553 6789 THIAMINE DEFICIENCY//THIAMINE//WERNICKES ENCEPHALOPATHY

Terms with highest relevance score



Rank Term Type of term Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
1 PYRIDOXINE DEPENDENT EPILEPSY Author keyword 38 89% 4% 17
2 PYRIDOXINE DEPENDENT SEIZURES Author keyword 38 89% 4% 17
3 ALDH7A1 Author keyword 15 68% 3% 13
4 METABOLIC EPILEPSY Author keyword 14 100% 2% 7
5 ANTIQUITIN Author keyword 12 52% 4% 16
6 ALDH7A1 GENE Author keyword 6 100% 1% 4
7 PYRIDOXINE DEPENDENCY Author keyword 3 100% 1% 3
8 ARMENIAN REPUBLICAN EPILEPSY EREBOUNI Address 2 67% 0% 2
9 B6 VITAMERS Author keyword 2 67% 0% 2
10 INFRAORBITAL NERVE CONSTRICTION Author keyword 2 67% 0% 2

Web of Science journal categories

Author Key Words



Rank Web of Science journal category Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
LCSH search Wikipedia search
1 PYRIDOXINE DEPENDENT EPILEPSY 38 89% 4% 17 Search PYRIDOXINE+DEPENDENT+EPILEPSY Search PYRIDOXINE+DEPENDENT+EPILEPSY
2 PYRIDOXINE DEPENDENT SEIZURES 38 89% 4% 17 Search PYRIDOXINE+DEPENDENT+SEIZURES Search PYRIDOXINE+DEPENDENT+SEIZURES
3 ALDH7A1 15 68% 3% 13 Search ALDH7A1 Search ALDH7A1
4 METABOLIC EPILEPSY 14 100% 2% 7 Search METABOLIC+EPILEPSY Search METABOLIC+EPILEPSY
5 ANTIQUITIN 12 52% 4% 16 Search ANTIQUITIN Search ANTIQUITIN
6 ALDH7A1 GENE 6 100% 1% 4 Search ALDH7A1+GENE Search ALDH7A1+GENE
7 PYRIDOXINE DEPENDENCY 3 100% 1% 3 Search PYRIDOXINE+DEPENDENCY Search PYRIDOXINE+DEPENDENCY
8 B6 VITAMERS 2 67% 0% 2 Search B6+VITAMERS Search B6+VITAMERS
9 INFRAORBITAL NERVE CONSTRICTION 2 67% 0% 2 Search INFRAORBITAL+NERVE+CONSTRICTION Search INFRAORBITAL+NERVE+CONSTRICTION
10 MILGAMMA 2 67% 0% 2 Search MILGAMMA Search MILGAMMA

Key Words Plus



Rank Web of Science journal category Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
1 RESPONSIVE SEIZURES 67 85% 9% 35
2 ANTIQUITIN ALDH7A1 45 94% 4% 16
3 ANTIQUITIN 28 69% 6% 24
4 ACID RESPONSIVE SEIZURES 17 100% 2% 8
5 ALPHA AMINOADIPIC SEMIALDEHYDE 8 70% 2% 7
6 PNPO DEFICIENCY 8 75% 1% 6
7 REDUCED NEED 8 100% 1% 5
8 PYRIDOXINE DEPENDENT EPILEPSY 7 37% 4% 16
9 ACUTE LUMBAGO 6 48% 2% 10
10 INTRAVENOUS PYRIDOXINE 6 80% 1% 4

Journals

Reviews



Title Publ. year Cit. Active
references
% act. ref.
to same field
Pyridoxine dependent epilepsy and antiquitin deficiency Clinical and molecular characteristics and recommendations for diagnosis, treatment and follow-up 2011 38 99 67%
Pyridoxine-dependent seizures: Findings from recent studies pose new questions 2002 31 40 80%
PYRIDOXINE-DEPENDENT SEIZURES, CLINICAL AND THERAPEUTIC ASPECTS 1991 58 7 100%
Epilepsy and inborn errors of metabolism in children 2009 17 20 40%
A relationship between analgesic and neurotropic effects by the example of milgamma 2012 0 5 100%
Current Treatment and Management of Pyridoxine-Dependent Epilepsy 2015 0 44 89%
Pyridoxine hydrochloride treatment of carpal tunnel syndrome: A review 2004 6 24 58%
VITAMIN-B6 SAFETY ISSUES 1990 31 3 67%
Vitamin B for treating peripheral neuropathy 2008 13 38 26%
Inborn errors of metabolism causing epilepsy 2013 7 72 13%

Address terms



Rank Address term Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ.
in class
1 ARMENIAN REPUBLICAN EPILEPSY EREBOUNI 2 67% 0.5% 2
2 C4N 1 50% 0.2% 1
3 CLIN PAEDIAT KIDNEY LIVER METAB DISORDERS 1 50% 0.2% 1
4 EPILEPSIEZENTRUM KINDER JUGENDL 1 50% 0.2% 1
5 EPILEPSY TREATMENT UNIT 1 50% 0.2% 1
6 FED STN ANIM PROD 1 50% 0.2% 1
7 HISTOL CYTOL CELLULAR BIOL 1 50% 0.2% 1
8 K LANS MED 1 50% 0.2% 1
9 KLIN CHEM ORDIAGNOST 1 50% 0.2% 1
10 MUHIMBILI HLTH SCI 1 50% 0.2% 1

Related classes at same level (level 1)



Rank Relatedness score Related classes
1 0.0000239691 MED PSYCHIAT DRUG ADDICT UNIT//ISONIAZID INTOXICATION//ZIPEPROL
2 0.0000210839 VITAMIN B 6//VITAMIN B 6 STATUS//4 PYRIDOXIC ACID
3 0.0000109468 LD PIPECOLIC ACID//PIPECOLIC ACID//L PIPECOLIC ACID
4 0.0000100055 SERINE BIOSYNTHESIS//PHOSPHORYLATED PATHWAY//3 PHOSPHOGLYCERATE DEHYDROGENASE
5 0.0000094155 WEST SYNDROME//INFANTILE SPASMS//HYPSARRHYTHMIA
6 0.0000074951 NONKETOTIC HYPERGLYCINEMIA//NON KETOTIC HYPERGLYCINEMIA//GLYCINE N ACYLTRANSFERASE
7 0.0000063116 AROMATIC L AMINO ACID DECARBOXYLASE DEFICIENCY//AROMATIC L AMINO ACID DECARBOXYLASE//L DOPA DECARBOXYLASE
8 0.0000062153 L 2 HYDROXYGLUTARIC ACIDURIA//GLUTARIC ACIDURIA TYPE I//GLUTARIC ACIDURIA TYPE 1
9 0.0000056202 HYPERPROLINEMIA//HYPERPROLINEMIA TYPE II//SUPERIOR MESENTERIC FLOW
10 0.0000055456 GABAA RECEPTOR CHLORIDE IONOPHORE COMPLEX//CEREBROSPINAL FLUID AND PLASMA LEVELS//FENGABINE