Class information for: |
Basic class information |
ID | Publications | Average number of references |
Avg. shr. active ref. in WoS |
---|---|---|---|
19464 | 439 | 21.8 | 65% |
Classes in level above (level 2) |
Terms with highest relevance score |
Rank | Term | Type of term | Relevance score (tfidf) |
Class's shr. of term's tot. occurrences |
Shr. of publ. in class containing term |
Num. of publ. in class |
---|---|---|---|---|---|---|
1 | ALAGILLE SYNDROME | Author keyword | 143 | 69% | 28% | 124 |
2 | ARTERIOHEPATIC DYSPLASIA | Author keyword | 27 | 83% | 3% | 15 |
3 | ALAGILLES SYNDROME | Author keyword | 21 | 85% | 3% | 11 |
4 | PAUCITY OF INTERLOBULAR BILE DUCTS | Author keyword | 18 | 89% | 2% | 8 |
5 | BILE DUCT PAUCITY | Author keyword | 9 | 83% | 1% | 5 |
6 | BUTTERFLY VERTEBRA | Author keyword | 8 | 62% | 2% | 8 |
7 | JAG1 | Author keyword | 7 | 34% | 4% | 17 |
8 | ALAGILLE | Author keyword | 4 | 75% | 1% | 3 |
9 | POSTERIOR EMBRYOTOXON | Author keyword | 4 | 56% | 1% | 5 |
10 | JAG1 GENE | Author keyword | 3 | 100% | 1% | 3 |
Web of Science journal categories |
Author Key Words |
Rank | Web of Science journal category | Relevance score (tfidf) |
Class's shr. of term's tot. occurrences |
Shr. of publ. in class containing term |
Num. of publ. in class |
LCSH search | Wikipedia search |
---|---|---|---|---|---|---|---|
1 | ALAGILLE SYNDROME | 143 | 69% | 28% | 124 | Search ALAGILLE+SYNDROME | Search ALAGILLE+SYNDROME |
2 | ARTERIOHEPATIC DYSPLASIA | 27 | 83% | 3% | 15 | Search ARTERIOHEPATIC+DYSPLASIA | Search ARTERIOHEPATIC+DYSPLASIA |
3 | ALAGILLES SYNDROME | 21 | 85% | 3% | 11 | Search ALAGILLES+SYNDROME | Search ALAGILLES+SYNDROME |
4 | PAUCITY OF INTERLOBULAR BILE DUCTS | 18 | 89% | 2% | 8 | Search PAUCITY+OF+INTERLOBULAR+BILE+DUCTS | Search PAUCITY+OF+INTERLOBULAR+BILE+DUCTS |
5 | BILE DUCT PAUCITY | 9 | 83% | 1% | 5 | Search BILE+DUCT+PAUCITY | Search BILE+DUCT+PAUCITY |
6 | BUTTERFLY VERTEBRA | 8 | 62% | 2% | 8 | Search BUTTERFLY+VERTEBRA | Search BUTTERFLY+VERTEBRA |
7 | JAG1 | 7 | 34% | 4% | 17 | Search JAG1 | Search JAG1 |
8 | ALAGILLE | 4 | 75% | 1% | 3 | Search ALAGILLE | Search ALAGILLE |
9 | POSTERIOR EMBRYOTOXON | 4 | 56% | 1% | 5 | Search POSTERIOR+EMBRYOTOXON | Search POSTERIOR+EMBRYOTOXON |
10 | JAG1 GENE | 3 | 100% | 1% | 3 | Search JAG1+GENE | Search JAG1+GENE |
Key Words Plus |
Rank | Web of Science journal category | Relevance score (tfidf) |
Class's shr. of term's tot. occurrences |
Shr. of publ. in class containing term |
Num. of publ. in class |
---|---|---|---|---|---|
1 | ARTERIOHEPATIC DYSPLASIA | 175 | 76% | 28% | 123 |
2 | INTERLOBULAR BILE DUCTS | 56 | 73% | 10% | 43 |
3 | PAUCITY | 53 | 58% | 14% | 61 |
4 | JAGGED1 GENE | 22 | 57% | 6% | 26 |
5 | SYNDROME ARTERIOHEPATIC DYSPLASIA | 19 | 80% | 3% | 12 |
6 | 20P | 15 | 68% | 3% | 13 |
7 | 20P12 | 11 | 100% | 1% | 6 |
8 | BUTTERFLY VERTEBRA | 9 | 83% | 1% | 5 |
9 | JAG1 MUTATIONS | 8 | 70% | 2% | 7 |
10 | SYNDROMIC PAUCITY | 6 | 71% | 1% | 5 |
Journals |
Reviews |
Title | Publ. year | Cit. | Active references |
% act. ref. to same field |
---|---|---|---|---|
Medical and dental management of Alagille syndrome: A review | 2014 | 1 | 15 | 93% |
Alagille Syndrome and Liver Transplantation | 2010 | 15 | 35 | 83% |
Medical Management of Alagille Syndrome | 2010 | 10 | 59 | 75% |
SYNDROMIC PAUCITY OF INTERLOBULAR BILE-DUCTS (ALAGILLE SYNDROME OR ARTERIOHEPATIC DYSPLASIA) - REVIEW OF 80 CASES | 1987 | 309 | 10 | 90% |
Alagille syndrome and the Jagged1 gene | 2001 | 52 | 44 | 80% |
Renal involvement and the role of Notch signalling in Alagille syndrome | 2013 | 2 | 67 | 66% |
Bile duct paucity in infancy | 2007 | 5 | 9 | 78% |
Alagille syndrome: case report with bilateral radio-ulnar synostosis and a literature review | 2003 | 6 | 7 | 100% |
Familial Translocation t(6;20)(p21;p13) Resulting in Partial Trisomy 6p and Partial Monosomy 20p: Report of a New Case and Review of the Literature | 2012 | 2 | 4 | 75% |
Hypertension and aortorenal disease in Alagille syndrome | 2012 | 2 | 39 | 69% |
Address terms |
Rank | Address term | Relevance score (tfidf) |
Class's shr. of term's tot. occurrences |
Shr. of publ. in class containing term |
Num. of publ. in class |
---|---|---|---|---|---|
1 | ABRAMSON 1006 | 1 | 50% | 0.5% | 2 |
2 | ABRAMSON 1007A | 1 | 50% | 0.5% | 2 |
3 | SERV HEPATOL PEDIAT | 1 | 10% | 1.6% | 7 |
4 | ANTHROPOL DATA BASE | 1 | 50% | 0.2% | 1 |
5 | DIP BIOL EVOLUZIONISTICA SPERIMENTALE | 1 | 50% | 0.2% | 1 |
6 | DIPARTIMENTO CHIRURG GEN TR IANTI ORGAN | 1 | 50% | 0.2% | 1 |
7 | DIPARTIMENTO SCI OSTET GINECOL PEDIAT | 1 | 50% | 0.2% | 1 |
8 | GASTROENTEROL HEPATOL NUTRPERELMAN MED | 1 | 50% | 0.2% | 1 |
9 | GENOME GENET DISORDERS | 1 | 50% | 0.2% | 1 |
10 | INSERMU56UNITE RECH HEPATOL PEDIAT | 1 | 50% | 0.2% | 1 |
Related classes at same level (level 1) |
Rank | Relatedness score | Related classes |
---|---|---|
1 | 0.0000154674 | BILIARY ATRESIA//KASAI OPERATION//PORTOENTEROSTOMY |
2 | 0.0000131907 | INTRAHEPATIC CHOLESTASIS OF PREGNANCY//PROGRESSIVE FAMILIAL INTRAHEPATIC CHOLESTASIS//ABCB11 |
3 | 0.0000079431 | NOTCH//NOTCH SIGNALING//NOTCH1 |
4 | 0.0000059286 | KABUKI SYNDROME//KABUKI MAKE UP SYNDROME//NIIKAWA KUROKI SYNDROME |
5 | 0.0000058417 | TRISOMY 10Q//MONOSOMY 10Q//10P TRISOMY |
6 | 0.0000050446 | MID AORTIC SYNDROME//MIDDLE AORTIC SYNDROME//MIDAORTIC SYNDROME |
7 | 0.0000044277 | CONGENITAL SCOLIOSIS//EARLY ONSET SCOLIOSIS//GROWING RODS |
8 | 0.0000042680 | MYELINATED RETINAL NERVE FIBERS//MYELINATED NERVE FIBERS//MYELINATED RETINAL NERVE FIBRES |
9 | 0.0000041326 | CHRONIC LIVER INSUFFICIENCY//HPPOLE MED//CHIRROSIS |
10 | 0.0000039285 | OPTIC NERVE HEAD DRUSEN//OPTIC DISC DRUSEN//OPTIC DISK DRUSEN |