Class information for:
Level 1: ALAGILLE SYNDROME//ARTERIOHEPATIC DYSPLASIA//ALAGILLES SYNDROME

Basic class information

ID Publications Average number
of references
Avg. shr. active
ref. in WoS
19464 439 21.8 65%



Bar chart of Publication_year

Last years might be incomplete

Classes in level above (level 2)



ID, lev.
above
Publications Label for level above
1798 5763 BILIARY ATRESIA//CADASIL//NOTCH3

Terms with highest relevance score



Rank Term Type of term Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
1 ALAGILLE SYNDROME Author keyword 143 69% 28% 124
2 ARTERIOHEPATIC DYSPLASIA Author keyword 27 83% 3% 15
3 ALAGILLES SYNDROME Author keyword 21 85% 3% 11
4 PAUCITY OF INTERLOBULAR BILE DUCTS Author keyword 18 89% 2% 8
5 BILE DUCT PAUCITY Author keyword 9 83% 1% 5
6 BUTTERFLY VERTEBRA Author keyword 8 62% 2% 8
7 JAG1 Author keyword 7 34% 4% 17
8 ALAGILLE Author keyword 4 75% 1% 3
9 POSTERIOR EMBRYOTOXON Author keyword 4 56% 1% 5
10 JAG1 GENE Author keyword 3 100% 1% 3

Web of Science journal categories

Author Key Words



Rank Web of Science journal category Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
LCSH search Wikipedia search
1 ALAGILLE SYNDROME 143 69% 28% 124 Search ALAGILLE+SYNDROME Search ALAGILLE+SYNDROME
2 ARTERIOHEPATIC DYSPLASIA 27 83% 3% 15 Search ARTERIOHEPATIC+DYSPLASIA Search ARTERIOHEPATIC+DYSPLASIA
3 ALAGILLES SYNDROME 21 85% 3% 11 Search ALAGILLES+SYNDROME Search ALAGILLES+SYNDROME
4 PAUCITY OF INTERLOBULAR BILE DUCTS 18 89% 2% 8 Search PAUCITY+OF+INTERLOBULAR+BILE+DUCTS Search PAUCITY+OF+INTERLOBULAR+BILE+DUCTS
5 BILE DUCT PAUCITY 9 83% 1% 5 Search BILE+DUCT+PAUCITY Search BILE+DUCT+PAUCITY
6 BUTTERFLY VERTEBRA 8 62% 2% 8 Search BUTTERFLY+VERTEBRA Search BUTTERFLY+VERTEBRA
7 JAG1 7 34% 4% 17 Search JAG1 Search JAG1
8 ALAGILLE 4 75% 1% 3 Search ALAGILLE Search ALAGILLE
9 POSTERIOR EMBRYOTOXON 4 56% 1% 5 Search POSTERIOR+EMBRYOTOXON Search POSTERIOR+EMBRYOTOXON
10 JAG1 GENE 3 100% 1% 3 Search JAG1+GENE Search JAG1+GENE

Key Words Plus



Rank Web of Science journal category Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
1 ARTERIOHEPATIC DYSPLASIA 175 76% 28% 123
2 INTERLOBULAR BILE DUCTS 56 73% 10% 43
3 PAUCITY 53 58% 14% 61
4 JAGGED1 GENE 22 57% 6% 26
5 SYNDROME ARTERIOHEPATIC DYSPLASIA 19 80% 3% 12
6 20P 15 68% 3% 13
7 20P12 11 100% 1% 6
8 BUTTERFLY VERTEBRA 9 83% 1% 5
9 JAG1 MUTATIONS 8 70% 2% 7
10 SYNDROMIC PAUCITY 6 71% 1% 5

Journals

Reviews



Title Publ. year Cit. Active
references
% act. ref.
to same field
Medical and dental management of Alagille syndrome: A review 2014 1 15 93%
Alagille Syndrome and Liver Transplantation 2010 15 35 83%
Medical Management of Alagille Syndrome 2010 10 59 75%
SYNDROMIC PAUCITY OF INTERLOBULAR BILE-DUCTS (ALAGILLE SYNDROME OR ARTERIOHEPATIC DYSPLASIA) - REVIEW OF 80 CASES 1987 309 10 90%
Alagille syndrome and the Jagged1 gene 2001 52 44 80%
Renal involvement and the role of Notch signalling in Alagille syndrome 2013 2 67 66%
Bile duct paucity in infancy 2007 5 9 78%
Alagille syndrome: case report with bilateral radio-ulnar synostosis and a literature review 2003 6 7 100%
Familial Translocation t(6;20)(p21;p13) Resulting in Partial Trisomy 6p and Partial Monosomy 20p: Report of a New Case and Review of the Literature 2012 2 4 75%
Hypertension and aortorenal disease in Alagille syndrome 2012 2 39 69%

Address terms



Rank Address term Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ.
in class
1 ABRAMSON 1006 1 50% 0.5% 2
2 ABRAMSON 1007A 1 50% 0.5% 2
3 SERV HEPATOL PEDIAT 1 10% 1.6% 7
4 ANTHROPOL DATA BASE 1 50% 0.2% 1
5 DIP BIOL EVOLUZIONISTICA SPERIMENTALE 1 50% 0.2% 1
6 DIPARTIMENTO CHIRURG GEN TR IANTI ORGAN 1 50% 0.2% 1
7 DIPARTIMENTO SCI OSTET GINECOL PEDIAT 1 50% 0.2% 1
8 GASTROENTEROL HEPATOL NUTRPERELMAN MED 1 50% 0.2% 1
9 GENOME GENET DISORDERS 1 50% 0.2% 1
10 INSERMU56UNITE RECH HEPATOL PEDIAT 1 50% 0.2% 1

Related classes at same level (level 1)



Rank Relatedness score Related classes
1 0.0000154674 BILIARY ATRESIA//KASAI OPERATION//PORTOENTEROSTOMY
2 0.0000131907 INTRAHEPATIC CHOLESTASIS OF PREGNANCY//PROGRESSIVE FAMILIAL INTRAHEPATIC CHOLESTASIS//ABCB11
3 0.0000079431 NOTCH//NOTCH SIGNALING//NOTCH1
4 0.0000059286 KABUKI SYNDROME//KABUKI MAKE UP SYNDROME//NIIKAWA KUROKI SYNDROME
5 0.0000058417 TRISOMY 10Q//MONOSOMY 10Q//10P TRISOMY
6 0.0000050446 MID AORTIC SYNDROME//MIDDLE AORTIC SYNDROME//MIDAORTIC SYNDROME
7 0.0000044277 CONGENITAL SCOLIOSIS//EARLY ONSET SCOLIOSIS//GROWING RODS
8 0.0000042680 MYELINATED RETINAL NERVE FIBERS//MYELINATED NERVE FIBERS//MYELINATED RETINAL NERVE FIBRES
9 0.0000041326 CHRONIC LIVER INSUFFICIENCY//HPPOLE MED//CHIRROSIS
10 0.0000039285 OPTIC NERVE HEAD DRUSEN//OPTIC DISC DRUSEN//OPTIC DISK DRUSEN