Class information for:
Level 1: ALVEOLAR CAPILLARY DYSPLASIA//PULMONARY INTERSTITIAL GLYCOGENOSIS//ABCA3

Basic class information

ID Publications Average number
of references
Avg. shr. active
ref. in WoS
18624 477 31.7 78%



Bar chart of Publication_year

Last years might be incomplete

Classes in level above (level 2)



ID, lev.
above
Publications Label for level above
994 9968 IDIOPATHIC PULMONARY FIBROSIS//USUAL INTERSTITIAL PNEUMONIA//PULMONARY ALVEOLAR PROTEINOSIS

Terms with highest relevance score



Rank Term Type of term Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
1 ALVEOLAR CAPILLARY DYSPLASIA Author keyword 76 85% 8% 40
2 PULMONARY INTERSTITIAL GLYCOGENOSIS Author keyword 21 90% 2% 9
3 ABCA3 Author keyword 17 52% 5% 23
4 MISALIGNMENT OF PULMONARY VEINS Author keyword 14 100% 1% 7
5 PEDIATRIC INTERSTITIAL LUNG DISEASE Author keyword 14 100% 1% 7
6 CONGENITAL ALVEOLAR CAPILLARY DYSPLASIA Author keyword 12 86% 1% 6
7 ACINAR DYSPLASIA Author keyword 8 100% 1% 5
8 CHRONIC PNEUMONITIS OF INFANCY Author keyword 8 100% 1% 5
9 MISALIGNMENT OF LUNG VESSELS Author keyword 8 100% 1% 5
10 MISALIGNMENT OF PULMONARY VESSELS Author keyword 8 100% 1% 5

Web of Science journal categories

Author Key Words



Rank Web of Science journal category Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
LCSH search Wikipedia search
1 ALVEOLAR CAPILLARY DYSPLASIA 76 85% 8% 40 Search ALVEOLAR+CAPILLARY+DYSPLASIA Search ALVEOLAR+CAPILLARY+DYSPLASIA
2 PULMONARY INTERSTITIAL GLYCOGENOSIS 21 90% 2% 9 Search PULMONARY+INTERSTITIAL+GLYCOGENOSIS Search PULMONARY+INTERSTITIAL+GLYCOGENOSIS
3 ABCA3 17 52% 5% 23 Search ABCA3 Search ABCA3
4 MISALIGNMENT OF PULMONARY VEINS 14 100% 1% 7 Search MISALIGNMENT+OF+PULMONARY+VEINS Search MISALIGNMENT+OF+PULMONARY+VEINS
5 PEDIATRIC INTERSTITIAL LUNG DISEASE 14 100% 1% 7 Search PEDIATRIC+INTERSTITIAL+LUNG+DISEASE Search PEDIATRIC+INTERSTITIAL+LUNG+DISEASE
6 CONGENITAL ALVEOLAR CAPILLARY DYSPLASIA 12 86% 1% 6 Search CONGENITAL+ALVEOLAR+CAPILLARY+DYSPLASIA Search CONGENITAL+ALVEOLAR+CAPILLARY+DYSPLASIA
7 ACINAR DYSPLASIA 8 100% 1% 5 Search ACINAR+DYSPLASIA Search ACINAR+DYSPLASIA
8 CHRONIC PNEUMONITIS OF INFANCY 8 100% 1% 5 Search CHRONIC+PNEUMONITIS+OF+INFANCY Search CHRONIC+PNEUMONITIS+OF+INFANCY
9 MISALIGNMENT OF LUNG VESSELS 8 100% 1% 5 Search MISALIGNMENT+OF+LUNG+VESSELS Search MISALIGNMENT+OF+LUNG+VESSELS
10 MISALIGNMENT OF PULMONARY VESSELS 8 100% 1% 5 Search MISALIGNMENT+OF+PULMONARY+VESSELS Search MISALIGNMENT+OF+PULMONARY+VESSELS

Key Words Plus



Rank Web of Science journal category Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
1 LUNG VESSELS 56 85% 6% 29
2 ABCA3 MUTATIONS 35 76% 5% 25
3 AFFECTED SIBLINGS 27 83% 3% 15
4 FATAL SURFACTANT DEFICIENCY 22 58% 5% 26
5 SURFACTANT DEFICIENCY 17 72% 3% 13
6 ALVEOLAR CAPILLARY DYSPLASIA 15 43% 6% 27
7 NEUROENDOCRINE CELL HYPERPLASIA 12 50% 4% 17
8 CAPILLARY DYSPLASIA 11 100% 1% 6
9 SFTPC 8 60% 2% 9
10 FAMILIAL PULMONARY FIBROSIS 8 100% 1% 5

Journals

Reviews



Title Publ. year Cit. Active references % act. ref.
to same field
Diseases of Pulmonary Surfactant Homeostasis 2015 2 120 31%
Interstitial lung disease in children 2014 4 48 79%
Alveolar Surfactant Homeostasis and the Pathogenesis of Pulmonary Disease 2010 90 65 25%
Interstitial lung disease in children 2011 10 26 73%
Alveolar capillary dysplasia - Report of a case of prolonged life without extracorporeal membrane oxygenation (ECMO) and review of the literature 2000 30 20 80%
Rapidly Fatal "Congenital Lung Dysplasia": A Case Report and Review of the Literature 2014 0 5 100%
Genetic Disorders of Surfactant Dysfunction 2009 44 180 31%
Evaluation and management of inherited disorders of surfactant metabolism 2010 7 31 61%
Diffuse lung disease of infancy: a pattern-based, algorithmic approach to histological diagnosis 2015 0 19 79%
Evaluating infants and children with interstitial lung disease 2007 15 57 53%

Address terms



Rank Address term Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
1 UMR S U938 4 67% 0.8% 4
2 PEDIAT PULM SECT 3 29% 2.1% 10
3 SECT NEONATOL PERINATAL PULM BIOL 2 24% 1.5% 7
4 MEMBER GERMAN LUNG DZL 1 100% 0.4% 2
5 PEDIATPEDIAT PULM SECT 1 100% 0.4% 2
6 GEN PEDIAT SECT 1 33% 0.4% 2
7 ABT KINDERKARDIOL PULMONOL 1 50% 0.2% 1
8 BERUGSGENOSSEN AFTLICHE KLINIKEN BERGMANNSHEIL 1 50% 0.2% 1
9 CATTEDRA CLIN PEDIAT 4 1 50% 0.2% 1
10 CINCINNATI CHILDRENS HOSP MED PULM BIOL 1 50% 0.2% 1

Related classes at same level (level 1)



Rank Relatedness score Related classes
1 0.0000174799 PULMONARY ALVEOLAR PROTEINOSIS//WHOLE LUNG LAVAGE//ALVEOLAR PROTEINOSIS
2 0.0000148568 IDIOPATHIC PULMONARY FIBROSIS//USUAL INTERSTITIAL PNEUMONIA//IDIOPATHIC INTERSTITIAL PNEUMONIA
3 0.0000141783 PULMONARY SURFACTANT//PULMONARY SURFACTANTS//RESPIRATORY DISTRESS SYNDROME
4 0.0000096175 SHRINKING LUNG SYNDROME//IDIOPATHIC PULMONARY HEMOSIDEROSIS//PULMONARY HEMOSIDEROSIS
5 0.0000085350 BRONCHIOLITIS OBLITERANS ORGANIZING PNEUMONIA//CRYPTOGENIC ORGANIZING PNEUMONIA//ORGANIZING PNEUMONIA
6 0.0000082129 SEGMENTAL INTESTINAL DILATATION//SEGMENTAL DILATATION//SEGMENTAL DILATATION OF ILEUM
7 0.0000079820 TTF 1//NAPSIN A//THYROID TRANSCRIPTION FACTOR 1
8 0.0000077753 FLEXIBLE BRONCHOSCOPY//OPEN LUNG BIOPSY//PULMONARY INFILTRATES
9 0.0000076645 PULMONARY AGENESIS//LUNG AGENESIS//PARTIAL TRISOMY 2P
10 0.0000071663 PULMONARY ALVEOLAR MICROLITHIASIS//SLC34A2 GENE//ALVEOLAR MICROLITHIASIS