Class information for: |
Basic class information |
ID | Publications | Average number of references |
Avg. shr. active ref. in WoS |
---|---|---|---|
16336 | 594 | 30.1 | 69% |
Classes in level above (level 2) |
ID, lev. above |
Publications | Label for level above |
---|---|---|
1442 | 7319 | MYASTHENIA GRAVIS//AGRIN//ACETYLCHOLINE RECEPTORS |
Terms with highest relevance score |
Rank | Term | Type of term | Relevance score (tfidf) |
Class's shr. of term's tot. occurrences |
Shr. of publ. in class containing term |
Num. of publ. in class |
---|---|---|---|---|---|---|
1 | CONGENITAL MYASTHENIC SYNDROME | Author keyword | 96 | 76% | 11% | 67 |
2 | CONGENITAL MYASTHENIC SYNDROMES | Author keyword | 54 | 72% | 7% | 42 |
3 | TUBULAR AGGREGATES | Author keyword | 35 | 72% | 5% | 28 |
4 | SLOW CHANNEL CONGENITAL MYASTHENIC SYNDROME | Author keyword | 21 | 90% | 2% | 9 |
5 | DOK7 | Author keyword | 17 | 79% | 2% | 11 |
6 | CONGENITAL MYASTHENIA | Author keyword | 17 | 63% | 3% | 17 |
7 | GFPT1 | Author keyword | 12 | 86% | 1% | 6 |
8 | LIMB GIRDLE MYASTHENIA | Author keyword | 12 | 86% | 1% | 6 |
9 | SLOW CHANNEL | Author keyword | 12 | 86% | 1% | 6 |
10 | SLOW CHANNEL SYNDROME | Author keyword | 11 | 67% | 2% | 10 |
Web of Science journal categories |
Author Key Words |
Rank | Web of Science journal category | Relevance score (tfidf) |
Class's shr. of term's tot. occurrences |
Shr. of publ. in class containing term |
Num. of publ. in class |
LCSH search | Wikipedia search |
---|---|---|---|---|---|---|---|
1 | CONGENITAL MYASTHENIC SYNDROME | 96 | 76% | 11% | 67 | Search CONGENITAL+MYASTHENIC+SYNDROME | Search CONGENITAL+MYASTHENIC+SYNDROME |
2 | CONGENITAL MYASTHENIC SYNDROMES | 54 | 72% | 7% | 42 | Search CONGENITAL+MYASTHENIC+SYNDROMES | Search CONGENITAL+MYASTHENIC+SYNDROMES |
3 | TUBULAR AGGREGATES | 35 | 72% | 5% | 28 | Search TUBULAR+AGGREGATES | Search TUBULAR+AGGREGATES |
4 | SLOW CHANNEL CONGENITAL MYASTHENIC SYNDROME | 21 | 90% | 2% | 9 | Search SLOW+CHANNEL+CONGENITAL+MYASTHENIC+SYNDROME | Search SLOW+CHANNEL+CONGENITAL+MYASTHENIC+SYNDROME |
5 | DOK7 | 17 | 79% | 2% | 11 | Search DOK7 | Search DOK7 |
6 | CONGENITAL MYASTHENIA | 17 | 63% | 3% | 17 | Search CONGENITAL+MYASTHENIA | Search CONGENITAL+MYASTHENIA |
7 | GFPT1 | 12 | 86% | 1% | 6 | Search GFPT1 | Search GFPT1 |
8 | LIMB GIRDLE MYASTHENIA | 12 | 86% | 1% | 6 | Search LIMB+GIRDLE+MYASTHENIA | Search LIMB+GIRDLE+MYASTHENIA |
9 | SLOW CHANNEL | 12 | 86% | 1% | 6 | Search SLOW+CHANNEL | Search SLOW+CHANNEL |
10 | SLOW CHANNEL SYNDROME | 11 | 67% | 2% | 10 | Search SLOW+CHANNEL+SYNDROME | Search SLOW+CHANNEL+SYNDROME |
Key Words Plus |
Rank | Web of Science journal category | Relevance score (tfidf) |
Class's shr. of term's tot. occurrences |
Shr. of publ. in class containing term |
Num. of publ. in class |
---|---|---|---|---|---|
1 | PLATE ACETYLCHOLINESTERASE DEFICIENCY | 85 | 85% | 8% | 45 |
2 | AGONIST BINDING AFFINITY | 46 | 63% | 8% | 46 |
3 | FAMILIAL INFANTILE MYASTHENIA | 35 | 86% | 3% | 18 |
4 | SECONDARY SYNAPTIC CLEFTS | 34 | 93% | 2% | 13 |
5 | SLOW CHANNEL SYNDROME | 34 | 69% | 5% | 29 |
6 | EPISODIC APNEA | 32 | 80% | 3% | 20 |
7 | NEUROMUSCULAR JUNCTION SYNAPTOPATHY | 31 | 73% | 4% | 24 |
8 | CHOLINE ACETYLTRANSFERASE MUTATIONS | 31 | 92% | 2% | 12 |
9 | CPSC SYNDROME | 31 | 92% | 2% | 12 |
10 | COLQ | 25 | 77% | 3% | 17 |
Journals |
Reviews |
Title | Publ. year | Cit. | Active references |
% act. ref. to same field |
---|---|---|---|---|
Congenital myasthenic syndromes: pathogenesis, diagnosis, and treatment | 2015 | 2 | 89 | 53% |
Current status of the congenital myasthenic syndromes | 2012 | 49 | 97 | 66% |
Current understanding of congenital myasthenic syndromes | 2005 | 91 | 68 | 65% |
Pharmacologic Treatment of Downstream of Tyrosine Kinase 7 Congenital Myasthenic Syndrome | 2014 | 5 | 22 | 82% |
The therapy of congenital myasthenic syndromes | 2007 | 45 | 40 | 65% |
Congenital Myasthenic Syndrome: A Brief Review | 2012 | 10 | 37 | 81% |
Congenital Myasthenic Syndromes: Current Diagnostic and Therapeutic Approaches | 2012 | 8 | 29 | 90% |
Congenital myasthenic syndromes - Recent advances | 1999 | 58 | 21 | 76% |
Therapeutic strategies in congenital myasthenic syndromes | 2008 | 17 | 26 | 92% |
Nicotinic acetylcholine receptors in human genetic disease | 2014 | 6 | 70 | 37% |
Address terms |
Rank | Address term | Relevance score (tfidf) |
Class's shr. of term's tot. occurrences |
Shr. of publ. in class containing term |
Num. of publ. in class |
---|---|---|---|---|---|
1 | UNITE FONCT CARDIOGENET MYOGENET | 5 | 55% | 1.0% | 6 |
2 | MUSCLE | 3 | 16% | 2.9% | 17 |
3 | NEUROL GERIATR MED PALLIAT CARE | 2 | 67% | 0.3% | 2 |
4 | RECEPTOR BIOL | 2 | 11% | 3.0% | 18 |
5 | UNITAT PATOL NEUROMUSCULAR | 1 | 31% | 0.7% | 4 |
6 | UNITE CLIN PATHOL MUSCULAIRE | 1 | 100% | 0.3% | 2 |
7 | SERV ELE OPHYSIOL | 1 | 30% | 0.5% | 3 |
8 | CHARITE FRAUEN KINDER JUGENDMED | 1 | 50% | 0.2% | 1 |
9 | CHILD NEUROL DEV PAEDIAT NEUROHABIL | 1 | 50% | 0.2% | 1 |
10 | CNRS URA 122 INSERM U25 | 1 | 50% | 0.2% | 1 |
Related classes at same level (level 1) |
Rank | Relatedness score | Related classes |
---|---|---|
1 | 0.0000178379 | MYASTHENIA GRAVIS//THYMECTOMY//EXPERIMENTAL AUTOIMMUNE MYASTHENIA GRAVIS |
2 | 0.0000176151 | AGRIN//NEUROMUSCULAR JUNCTION//ACETYLCHOLINE RECEPTORS |
3 | 0.0000115848 | DS DNA ANTIBODIES//INTERNAL AUTOIMMUNE METAB DIS//CHU PITIE SALPETRIERE HP |
4 | 0.0000109886 | ARTHROGRYPOSIS//NEU LAXOVA SYNDROME//AMYOPLASIA |
5 | 0.0000099859 | CHAIR BIOPHYS MOL NEUROBIOL//NICOTINIC ACETYLCHOLINE RECEPTOR//CYS LOOP RECEPTORS |
6 | 0.0000066814 | PERIODIC PARALYSIS//THYROTOXIC PERIODIC PARALYSIS//HYPOKALEMIC PERIODIC PARALYSIS |
7 | 0.0000064122 | NEMALINE MYOPATHY//CONGENITAL MYOPATHY//CENTRONUCLEAR MYOPATHY |
8 | 0.0000050783 | ELECTRICAL IMPEDANCE MYOGRAPHY//MUSCLE ULTRASOUND//CENTRAL HYPOTONIA |
9 | 0.0000047830 | CONGENITAL DISORDERS OF GLYCOSYLATION//CARBOHYDRATE DEFICIENT GLYCOPROTEIN SYNDROME//CDG |
10 | 0.0000047281 | ACETYLCHOLINESTERASE//BUTYRYLCHOLINESTERASE//MOLECULAR FORMS |