Class information for:
Level 1: CHOLESTERYL ESTER STORAGE DISEASE//LYSOSOMAL ACID LIPASE//WOLMAN DISEASE

Basic class information

ID Publications Average number
of references
Avg. shr. active
ref. in WoS
15364 646 29.4 49%



Bar chart of Publication_year

Last years might be incomplete

Classes in level above (level 2)



ID, lev.
above
Publications Label for level above
759 11731 PLANT STEROLS//PHYTOSTEROLS//SITOSTANOL

Terms with highest relevance score



Rank Term Type of term Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
1 CHOLESTERYL ESTER STORAGE DISEASE Author keyword 99 97% 4% 29
2 LYSOSOMAL ACID LIPASE Author keyword 61 78% 6% 40
3 WOLMAN DISEASE Author keyword 53 85% 4% 28
4 CHOLESTEROL ESTER STORAGE DISEASE Author keyword 20 100% 1% 9
5 LYSOSOMAL ACID LIPASE DEFICIENCY Author keyword 17 100% 1% 8
6 WOLMANS DISEASE Author keyword 11 100% 1% 6
7 ACID LIPASE Author keyword 8 56% 2% 10
8 NEUTRAL CHOLESTEROL ESTERASE Author keyword 7 67% 1% 6
9 CHOLESTERYL ESTER HYDROLYSIS Author keyword 5 50% 1% 7
10 CHOLESTERYL ESTER HYDROLASE Author keyword 4 36% 2% 10

Web of Science journal categories

Author Key Words



Rank Web of Science journal category Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
LCSH search Wikipedia search
1 CHOLESTERYL ESTER STORAGE DISEASE 99 97% 4% 29 Search CHOLESTERYL+ESTER+STORAGE+DISEASE Search CHOLESTERYL+ESTER+STORAGE+DISEASE
2 LYSOSOMAL ACID LIPASE 61 78% 6% 40 Search LYSOSOMAL+ACID+LIPASE Search LYSOSOMAL+ACID+LIPASE
3 WOLMAN DISEASE 53 85% 4% 28 Search WOLMAN+DISEASE Search WOLMAN+DISEASE
4 CHOLESTEROL ESTER STORAGE DISEASE 20 100% 1% 9 Search CHOLESTEROL+ESTER+STORAGE+DISEASE Search CHOLESTEROL+ESTER+STORAGE+DISEASE
5 LYSOSOMAL ACID LIPASE DEFICIENCY 17 100% 1% 8 Search LYSOSOMAL+ACID+LIPASE+DEFICIENCY Search LYSOSOMAL+ACID+LIPASE+DEFICIENCY
6 WOLMANS DISEASE 11 100% 1% 6 Search WOLMANS+DISEASE Search WOLMANS+DISEASE
7 ACID LIPASE 8 56% 2% 10 Search ACID+LIPASE Search ACID+LIPASE
8 NEUTRAL CHOLESTEROL ESTERASE 7 67% 1% 6 Search NEUTRAL+CHOLESTEROL+ESTERASE Search NEUTRAL+CHOLESTEROL+ESTERASE
9 CHOLESTERYL ESTER HYDROLYSIS 5 50% 1% 7 Search CHOLESTERYL+ESTER+HYDROLYSIS Search CHOLESTERYL+ESTER+HYDROLYSIS
10 CHOLESTERYL ESTER HYDROLASE 4 36% 2% 10 Search CHOLESTERYL+ESTER+HYDROLASE Search CHOLESTERYL+ESTER+HYDROLASE

Key Words Plus



Rank Web of Science journal category Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
1 WOLMAN DISEASE 63 83% 5% 35
2 SPLICE JUNCTION MUTATION 31 76% 3% 22
3 CESD 31 92% 2% 12
4 ESTER STORAGE DISEASE 28 57% 5% 33
5 LYSOSOMAL ACID LIPASE 27 47% 7% 42
6 WOLMANS DISEASE 10 73% 1% 8
7 LAL MICE 8 100% 1% 5
8 EMR1A 212D RECOGNIZING SITE 6 100% 1% 4
9 SUBCLINICAL COURSE 4 75% 0% 3
10 WOLMAN 4 75% 0% 3

Journals

Reviews



Title Publ. year Cit. Active references % act. ref.
to same field
Cholesteryl ester storage disease: Review of the findings in 135 reported patients with an underdiagnosed disease 2013 22 89 90%
Lysosomal acid lipase deficiency - An under-recognized cause of dyslipidaemia and liver dysfunction 2014 8 64 64%
Regulation of Lipid Droplet Cholesterol Efflux From Macrophage Foam Cells 2012 38 49 37%
Macrophage cholesteryl ester mobilization and atherosclerosis 2010 41 70 44%
Lysosomal acid lipase A and the hypercholesterolaemic phenotype 2013 12 55 47%
Early steps in reverse cholesterol transport: cholesteryl ester hydrolase and other hydrolases 2012 5 41 44%
WOLMAN-DISEASE AND ITS TREATMENT 1995 15 31 68%
The Role of Neutral Cholesterol Ester Hydrolysis in Macrophage Foam Cells 2011 9 44 25%
Overexpression of lysosomal acid lipase and other proteins in atherosclerosis 2006 13 124 19%
Lysosomal acid lipase and atherosclerosis 2004 12 37 32%

Address terms



Rank Address term Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ.
in class
1 MED HLTH SCI NUTR 2 67% 0.3% 2
2 HLTH TECHNOL BIOCHEM 1 100% 0.3% 2
3 IU SIMON CANC 1 15% 1.2% 8
4 ARIZONA HLTH SCI RADIOL 1 50% 0.2% 1
5 HEMATOL ONCOL BLOOD BONE MARROW TRANSPLANTA 1 50% 0.2% 1
6 IST SCI SAN RAFFAELE HOSP 1 50% 0.2% 1
7 LIPID SCI SECT 1 50% 0.2% 1
8 OR WELF COOPERAT 1 50% 0.2% 1
9 ARIZONA HLTH SCI CHILDRENS 0 33% 0.2% 1
10 BIOCHIM MED MALAD METAB 0 33% 0.2% 1

Related classes at same level (level 1)



Rank Relatedness score Related classes
1 0.0000172172 ACAT INHIBITOR//ARTERIOSCLEROSIS PROGRAM//ACYL COA CHOLESTEROL ACYLTRANSFERASE ACAT
2 0.0000167104 BILE SALT DEPENDENT LIPASE//CHOLESTEROL ESTERASE//CARBAMATE INHIBITORS
3 0.0000150741 CONTINUOUS NORMOBARIC HYPOXIA//BIOMED SCI DALTON CARDIOVASC//GLUTATHIONE RELATED ENZYME
4 0.0000145719 FARBER DISEASE//ASAH1//FARBER LIPOGRANULOMATOSIS
5 0.0000126979 AGE RELATED DECREASE IN PGI2 PRODUCTION//EN FACE TECHNIQUE//15 ISOPROSTANE F 2T
6 0.0000097175 PERILIPIN//LIPID DROPLET//ADIPOSE TRIGLYCERIDE LIPASE
7 0.0000084610 ELECTRONEGATIVE LDL//ELECTRONEGATIVE LOW DENSITY LIPOPROTEIN//ENZYMATICALLY MODIFIED LDL
8 0.0000073117 CARBOXYLESTERASE//DRUG METAB BIOPHARMACEUT//CARBOXYLESTERASES
9 0.0000063670 SCAVENGER RECEPTOR//FRACTIONATED H 3HEPARIN//CLASS A SCAVENGER RECEPTOR
10 0.0000061877 ANTIOXIDANT PHARMACOL//NITROSONIFEDIPINE//MYOCYTE MIGRATION