Class information for:
Level 1: ADRENOLEUKODYSTROPHY//ADRENOMYELONEUROPATHY//X LINKED ADRENOLEUKODYSTROPHY

Basic class information

ID Publications Average number
of references
Avg. shr. active
ref. in WoS
10384 1002 30.2 74%



Bar chart of Publication_year

Last years might be incomplete

Classes in level above (level 2)



ID, lev.
above
Publications Label for level above
1385 7668 ADRENOLEUKODYSTROPHY//FATTY ACID BINDING PROTEIN//X LINKED ADRENOLEUKODYSTROPHY

Terms with highest relevance score



Rank Term Type of term Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
1 ADRENOLEUKODYSTROPHY Author keyword 264 73% 20% 203
2 ADRENOMYELONEUROPATHY Author keyword 122 88% 6% 58
3 X LINKED ADRENOLEUKODYSTROPHY Author keyword 98 75% 7% 71
4 ABCD1 Author keyword 72 91% 3% 30
5 X ALD Author keyword 41 81% 2% 25
6 LORENZOS OIL Author keyword 35 89% 2% 16
7 ABCD1 GENE Author keyword 33 100% 1% 13
8 VERY LONG CHAIN FATTY ACIDS Author keyword 25 34% 6% 61
9 ALDP Author keyword 21 90% 1% 9
10 NEUROMETAB DIS Address 13 58% 1% 15

Web of Science journal categories

Author Key Words



Rank Web of Science journal category Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
LCSH search Wikipedia search
1 ADRENOLEUKODYSTROPHY 264 73% 20% 203 Search ADRENOLEUKODYSTROPHY Search ADRENOLEUKODYSTROPHY
2 ADRENOMYELONEUROPATHY 122 88% 6% 58 Search ADRENOMYELONEUROPATHY Search ADRENOMYELONEUROPATHY
3 X LINKED ADRENOLEUKODYSTROPHY 98 75% 7% 71 Search X+LINKED+ADRENOLEUKODYSTROPHY Search X+LINKED+ADRENOLEUKODYSTROPHY
4 ABCD1 72 91% 3% 30 Search ABCD1 Search ABCD1
5 X ALD 41 81% 2% 25 Search X+ALD Search X+ALD
6 LORENZOS OIL 35 89% 2% 16 Search LORENZOS+OIL Search LORENZOS+OIL
7 ABCD1 GENE 33 100% 1% 13 Search ABCD1+GENE Search ABCD1+GENE
8 VERY LONG CHAIN FATTY ACIDS 25 34% 6% 61 Search VERY+LONG+CHAIN+FATTY+ACIDS Search VERY+LONG+CHAIN+FATTY+ACIDS
9 ALDP 21 90% 1% 9 Search ALDP Search ALDP
10 ADRENOLEUKODYSTROPHY PROTEIN 12 86% 1% 6 Search ADRENOLEUKODYSTROPHY+PROTEIN Search ADRENOLEUKODYSTROPHY+PROTEIN

Key Words Plus



Rank Web of Science journal category Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
1 ADRENOMYELONEUROPATHY 288 87% 14% 141
2 X LINKED ADRENOLEUKODYSTROPHY 151 41% 28% 284
3 CHILDHOOD ADRENOLEUKODYSTROPHY 97 82% 6% 56
4 ALD GENE 75 91% 3% 31
5 LINKED ADRENOLEUKODYSTROPHY 67 89% 3% 31
6 ADRENO LEUKODYSTROPHY 57 79% 4% 37
7 CEREBRAL ADRENOLEUKODYSTROPHY 53 95% 2% 18
8 PEROXISOMAL MEMBRANE PROTEIN 50 57% 6% 60
9 LORENZO OIL 47 84% 3% 26
10 PROBABLE VARIANT 38 93% 1% 14

Journals

Reviews



Title Publ. year Cit. Active references % act. ref.
to same field
X-linked adrenoleukodystrophy 2007 105 86 86%
X-linked adrenoleukodystrophy: Clinical, metabolic, genetic and pathophysiological aspects 2012 39 93 73%
X-linked adrenoleukodystrophy: Clinical, biochemical and pathogenetic aspects 2006 64 113 81%
Pathophysiology of X-linked adrenoleukodystrophy 2014 7 85 84%
X-linked adrenoleukodystrophy (X-ALD): clinical presentation and guidelines for diagnosis, follow-up and management 2012 23 61 79%
Adrenoleukodystrophy: phenotype, genetics, pathogenesis and therapy 1997 222 127 72%
Peroxisomal ABC transporters: Structure, function and role in disease 2012 30 109 50%
X-linked adrenoleukodystrophy: Overview and prognosis as a function of age and brain magnetic resonance imaging abnormality. A study involving 372 patients 2000 53 66 89%
Adrenoleukodystrophy in female heterozygotes: Underrecognized and undertreated 2012 12 61 87%
The peroxisomal ABC transporter family 2007 50 93 59%

Address terms



Rank Address term Relevance score
(tfidf)
Class's shr.
of term's tot.
occurrences
Shr. of publ.
in class containing
term
Num. of
publ. in
class
1 NEUROMETAB DIS 13 58% 1.5% 15
2 CLIN CHEM METAB 11 78% 0.7% 7
3 NEUROMETABOL DIS 7 67% 0.6% 6
4 MOL DIAG GENET DIS 5 60% 0.6% 6
5 DARBY CHILDREN 4 67% 0.4% 4
6 NEUROPATOL BELLVITGE 3 100% 0.3% 3
7 EA7270 3 42% 0.5% 5
8 BIOMED NEURODEGENERAT DIS CIBERNED 2 67% 0.2% 2
9 BIOPEROXIL BIOCHIM PEROXYSOME INFLAMMAT MET 2 67% 0.2% 2
10 DIP SCI NEUROL VIS 2 67% 0.2% 2

Related classes at same level (level 1)



Rank Relatedness score Related classes
1 0.0000272672 PHYTANIC ACID//ZELLWEGER SYNDROME//RHIZOMELIC CHONDRODYSPLASIA PUNCTATA
2 0.0000096168 ALEXANDER DISEASE//LEUKODYSTROPHY//VANISHING WHITE MATTER DISEASE
3 0.0000089889 GLOBOID CELL LEUKODYSTROPHY//KRABBE DISEASE//PSYCHOSINE
4 0.0000070593 PEROXIN//PEROXISOME BIOGENESIS//PEROXISOME
5 0.0000068170 ACYL COA SYNTHETASE//FATTY ACID TRANSPORT PROTEIN//FATP
6 0.0000055371 METACHROMATIC LEUKODYSTROPHY//ARYLSULFATASE A//MULTIPLE SULFATASE DEFICIENCY
7 0.0000046698 KLUVER BUCY SYNDROME//HYPERORALITY//POSTICTAL BEHAVIOR
8 0.0000030199 TRIPLE A SYNDROME//ALACRIMA//ALLGROVE SYNDROME
9 0.0000024873 ELOVL4//STGD3//2 HYDROXY FATTY ACIDS
10 0.0000024147 TRANSALDOLASE DEFICIENCY//ESA 8080//NEONATAL HAEMORRHAGIC DIATHESIS