Class information for: |
Basic class information |
ID | Publications | Average number of references |
Avg. shr. active ref. in WoS |
---|---|---|---|
10384 | 1002 | 30.2 | 74% |
Classes in level above (level 2) |
ID, lev. above |
Publications | Label for level above |
---|---|---|
1385 | 7668 | ADRENOLEUKODYSTROPHY//FATTY ACID BINDING PROTEIN//X LINKED ADRENOLEUKODYSTROPHY |
Terms with highest relevance score |
Rank | Term | Type of term | Relevance score (tfidf) |
Class's shr. of term's tot. occurrences |
Shr. of publ. in class containing term |
Num. of publ. in class |
---|---|---|---|---|---|---|
1 | ADRENOLEUKODYSTROPHY | Author keyword | 264 | 73% | 20% | 203 |
2 | ADRENOMYELONEUROPATHY | Author keyword | 122 | 88% | 6% | 58 |
3 | X LINKED ADRENOLEUKODYSTROPHY | Author keyword | 98 | 75% | 7% | 71 |
4 | ABCD1 | Author keyword | 72 | 91% | 3% | 30 |
5 | X ALD | Author keyword | 41 | 81% | 2% | 25 |
6 | LORENZOS OIL | Author keyword | 35 | 89% | 2% | 16 |
7 | ABCD1 GENE | Author keyword | 33 | 100% | 1% | 13 |
8 | VERY LONG CHAIN FATTY ACIDS | Author keyword | 25 | 34% | 6% | 61 |
9 | ALDP | Author keyword | 21 | 90% | 1% | 9 |
10 | NEUROMETAB DIS | Address | 13 | 58% | 1% | 15 |
Web of Science journal categories |
Author Key Words |
Rank | Web of Science journal category | Relevance score (tfidf) |
Class's shr. of term's tot. occurrences |
Shr. of publ. in class containing term |
Num. of publ. in class |
LCSH search | Wikipedia search |
---|---|---|---|---|---|---|---|
1 | ADRENOLEUKODYSTROPHY | 264 | 73% | 20% | 203 | Search ADRENOLEUKODYSTROPHY | Search ADRENOLEUKODYSTROPHY |
2 | ADRENOMYELONEUROPATHY | 122 | 88% | 6% | 58 | Search ADRENOMYELONEUROPATHY | Search ADRENOMYELONEUROPATHY |
3 | X LINKED ADRENOLEUKODYSTROPHY | 98 | 75% | 7% | 71 | Search X+LINKED+ADRENOLEUKODYSTROPHY | Search X+LINKED+ADRENOLEUKODYSTROPHY |
4 | ABCD1 | 72 | 91% | 3% | 30 | Search ABCD1 | Search ABCD1 |
5 | X ALD | 41 | 81% | 2% | 25 | Search X+ALD | Search X+ALD |
6 | LORENZOS OIL | 35 | 89% | 2% | 16 | Search LORENZOS+OIL | Search LORENZOS+OIL |
7 | ABCD1 GENE | 33 | 100% | 1% | 13 | Search ABCD1+GENE | Search ABCD1+GENE |
8 | VERY LONG CHAIN FATTY ACIDS | 25 | 34% | 6% | 61 | Search VERY+LONG+CHAIN+FATTY+ACIDS | Search VERY+LONG+CHAIN+FATTY+ACIDS |
9 | ALDP | 21 | 90% | 1% | 9 | Search ALDP | Search ALDP |
10 | ADRENOLEUKODYSTROPHY PROTEIN | 12 | 86% | 1% | 6 | Search ADRENOLEUKODYSTROPHY+PROTEIN | Search ADRENOLEUKODYSTROPHY+PROTEIN |
Key Words Plus |
Rank | Web of Science journal category | Relevance score (tfidf) |
Class's shr. of term's tot. occurrences |
Shr. of publ. in class containing term |
Num. of publ. in class |
---|---|---|---|---|---|
1 | ADRENOMYELONEUROPATHY | 288 | 87% | 14% | 141 |
2 | X LINKED ADRENOLEUKODYSTROPHY | 151 | 41% | 28% | 284 |
3 | CHILDHOOD ADRENOLEUKODYSTROPHY | 97 | 82% | 6% | 56 |
4 | ALD GENE | 75 | 91% | 3% | 31 |
5 | LINKED ADRENOLEUKODYSTROPHY | 67 | 89% | 3% | 31 |
6 | ADRENO LEUKODYSTROPHY | 57 | 79% | 4% | 37 |
7 | CEREBRAL ADRENOLEUKODYSTROPHY | 53 | 95% | 2% | 18 |
8 | PEROXISOMAL MEMBRANE PROTEIN | 50 | 57% | 6% | 60 |
9 | LORENZO OIL | 47 | 84% | 3% | 26 |
10 | PROBABLE VARIANT | 38 | 93% | 1% | 14 |
Journals |
Reviews |
Title | Publ. year | Cit. | Active references | % act. ref. to same field |
---|---|---|---|---|
X-linked adrenoleukodystrophy | 2007 | 105 | 86 | 86% |
X-linked adrenoleukodystrophy: Clinical, metabolic, genetic and pathophysiological aspects | 2012 | 39 | 93 | 73% |
X-linked adrenoleukodystrophy: Clinical, biochemical and pathogenetic aspects | 2006 | 64 | 113 | 81% |
Pathophysiology of X-linked adrenoleukodystrophy | 2014 | 7 | 85 | 84% |
X-linked adrenoleukodystrophy (X-ALD): clinical presentation and guidelines for diagnosis, follow-up and management | 2012 | 23 | 61 | 79% |
Adrenoleukodystrophy: phenotype, genetics, pathogenesis and therapy | 1997 | 222 | 127 | 72% |
Peroxisomal ABC transporters: Structure, function and role in disease | 2012 | 30 | 109 | 50% |
X-linked adrenoleukodystrophy: Overview and prognosis as a function of age and brain magnetic resonance imaging abnormality. A study involving 372 patients | 2000 | 53 | 66 | 89% |
Adrenoleukodystrophy in female heterozygotes: Underrecognized and undertreated | 2012 | 12 | 61 | 87% |
The peroxisomal ABC transporter family | 2007 | 50 | 93 | 59% |
Address terms |
Rank | Address term | Relevance score (tfidf) |
Class's shr. of term's tot. occurrences |
Shr. of publ. in class containing term |
Num. of publ. in class |
---|---|---|---|---|---|
1 | NEUROMETAB DIS | 13 | 58% | 1.5% | 15 |
2 | CLIN CHEM METAB | 11 | 78% | 0.7% | 7 |
3 | NEUROMETABOL DIS | 7 | 67% | 0.6% | 6 |
4 | MOL DIAG GENET DIS | 5 | 60% | 0.6% | 6 |
5 | DARBY CHILDREN | 4 | 67% | 0.4% | 4 |
6 | NEUROPATOL BELLVITGE | 3 | 100% | 0.3% | 3 |
7 | EA7270 | 3 | 42% | 0.5% | 5 |
8 | BIOMED NEURODEGENERAT DIS CIBERNED | 2 | 67% | 0.2% | 2 |
9 | BIOPEROXIL BIOCHIM PEROXYSOME INFLAMMAT MET | 2 | 67% | 0.2% | 2 |
10 | DIP SCI NEUROL VIS | 2 | 67% | 0.2% | 2 |
Related classes at same level (level 1) |
Rank | Relatedness score | Related classes |
---|---|---|
1 | 0.0000272672 | PHYTANIC ACID//ZELLWEGER SYNDROME//RHIZOMELIC CHONDRODYSPLASIA PUNCTATA |
2 | 0.0000096168 | ALEXANDER DISEASE//LEUKODYSTROPHY//VANISHING WHITE MATTER DISEASE |
3 | 0.0000089889 | GLOBOID CELL LEUKODYSTROPHY//KRABBE DISEASE//PSYCHOSINE |
4 | 0.0000070593 | PEROXIN//PEROXISOME BIOGENESIS//PEROXISOME |
5 | 0.0000068170 | ACYL COA SYNTHETASE//FATTY ACID TRANSPORT PROTEIN//FATP |
6 | 0.0000055371 | METACHROMATIC LEUKODYSTROPHY//ARYLSULFATASE A//MULTIPLE SULFATASE DEFICIENCY |
7 | 0.0000046698 | KLUVER BUCY SYNDROME//HYPERORALITY//POSTICTAL BEHAVIOR |
8 | 0.0000030199 | TRIPLE A SYNDROME//ALACRIMA//ALLGROVE SYNDROME |
9 | 0.0000024873 | ELOVL4//STGD3//2 HYDROXY FATTY ACIDS |
10 | 0.0000024147 | TRANSALDOLASE DEFICIENCY//ESA 8080//NEONATAL HAEMORRHAGIC DIATHESIS |